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Bryan Winchester

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Chemicals & Drugs

Anatomy

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Glycosylation

Disorders

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TOP 3
Andreas Gal; Derralynn A Hughes; Bryan Winchester
Toward a consensus in the laboratory diagnostics of Fabry disease - recommendations of a European expert group.
Clare E Beesley; Elisabeth P Young; Niamh Finnegan; Marie Jackson; Kevin Mills; Ashok Vellodi; Maureen Cleary; Bryan Winchester
Discovery of a new biomarker for the mucopolysaccharidoses (MPS), dipeptidyl peptidase IV (DPP-IV; CD26), by SELDI-TOF mass spectrometry.
François Foulquier; Daniel Ungar; Ellen Reynders; Renate Zeevaert; Philippa Mills; Maria Teresa García-Silva; Paz Briones; Bryan Winchester; Willy Morelle; Monty Krieger; Willem ANNAERT; Gert Matthijs
A new inborn error of glycosylation due to a Cog8 deficiency reveals a critical role for the Cog1-Cog8 interaction in COG complex formation.

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All Publications

2011: Andreas Gal; Derralynn A Hughes; Bryan Winchester
Toward a consensus in the laboratory diagnostics of Fabry disease - recommendations of a European expert group.
Journal of inherited metabolic disease 2011;34(2):509-14.
2009: Clare E Beesley; Elisabeth P Young; Niamh Finnegan; Marie Jackson; Kevin Mills; Ashok Vellodi; Maureen Cleary; Bryan Winchester
Discovery of a new biomarker for the mucopolysaccharidoses (MPS), dipeptidyl peptidase IV (DPP-IV; CD26), by SELDI-TOF mass spectrometry.
Molecular genetics and metabolism 2009;96(4):218-24.
2007: François Foulquier; Daniel Ungar; Ellen Reynders; Renate Zeevaert; Philippa Mills; Maria Teresa García-Silva; Paz Briones; Bryan Winchester; Willy Morelle; Monty Krieger; Willem ANNAERT; Gert Matthijs
A new inborn error of glycosylation due to a Cog8 deficiency reveals a critical role for the Cog1-Cog8 interaction in COG complex formation.
Human molecular genetics 2007;16(7):717-30.
2007: Clare E Beesley; Daniela Concolino; Mirella Filocamo; Bryan Winchester; Pietro Strisciuglio
Identification and characterisation of an 8.7 kb deletion and a novel nonsense mutation in two Italian families with Sanfilippo syndrome type D (mucopolysaccharidosis IIID).
Molecular genetics and metabolism 2007;90(1):77-80.
2006: Janice L Holton; Clare E Beesley; Marie Jackson; K Venner; N Bhardwaj; Bryan Winchester; A Al-Memar
Autophagic vacuolar myopathy in twin girls.
Neuropathology and applied neurobiology 2006;32(3):253-9.
2006: Gabriel Chow; Clare E Beesley; Keith Robson; Bryan Winchester; Janice L Holton
Case of X-linked myopathy with excessive autophagy.
Journal of child neurology 2006;21(5):431-3.
2006: Kevin Mills; Philippa Mills; Marie Jackson; Viki Worthington; Clare E Beesley; Anúska Mann; Peter Clayton; Stephanie Grunewald; Geoffrey Keir; Liz Young; James Langridge; Nasi Mian; Bryan Winchester
Diagnosis of congenital disorders of glycosylation type-I using protein chip technology.
Proteomics 2006;6(7):2295-304.
2006: François Foulquier; Eliza Vasile; Els Schollen; Nico Callewaert; Tim Raemaekers; Dulce Quelhas; Jaak Jaeken; Philippa Mills; Bryan Winchester; Monty Krieger; Willem ANNAERT; Gert Matthijs
Conserved oligomeric Golgi complex subunit 1 deficiency reveals a previously uncharacterized congenital disorder of glycosylation type II.
Proceedings of the National Academy of Sciences of the United States of America 2006;103(10):3764-9.
2005: Suzan Wopereis; Eva Morava; Stephanie Grünewald; Philippa B Mills; Bryan Winchester; Peter Clayton; Paul Coucke; Karin M L C Huijben; Ron A Wevers
A combined defect in the biosynthesis of N- and O-glycans in patients with cutis laxa and neurological involvement: the biochemical characteristics.
Biochimica et biophysica acta 2005;1741(1-2):156-64.
2005: Elisabeth Young; Kevin Mills; Peter Morris; Ashok Vellodi; P Lee; S Waldek; Bryan Winchester
Is globotriaosylceramide a useful biomarker in Fabry disease?
Acta paediatrica (Oslo, Norway : 1992). Supplement 2005;94(447):51-4; discussion 37-8.
2005: Marie Jackson; Peter Clayton; S Grunewald; Geoffrey Keir; Kevin Mills; Philippa Mills; Bryan Winchester; Viki Worthington; E Young
Elevation of plasma aspartylglucosaminidase is a useful marker for the congenital disorders of glycosylation type I (CDG I).
Journal of inherited metabolic disease 2005;28(6):1197-8.
2005: Clare E Beesley; Marie Jackson; EP Young; Ashok Vellodi; Bryan Winchester
Molecular defects in Sanfilippo syndrome type B (mucopolysaccharidosis IIIB).
Journal of inherited metabolic disease 2005;28(5):759-67.
2005: Kevin Mills; Simon Eaton; Victoria Ledger; Elisabeth Young; Bryan Winchester
The synthesis of internal standards for the quantitative determination of sphingolipids by tandem mass spectrometry.
Rapid communications in mass spectrometry : RCM 2005;19(12):1739-48.
2005: Kevin Mills; Peter Morris; P Lee; Ashok Vellodi; S Waldek; Elisabeth Young; Bryan Winchester
Measurement of urinary CDH and CTH by tandem mass spectrometry in patients hemizygous and heterozygous for Fabry disease.
Journal of inherited metabolic disease 2005;28(1):35-48.
2004: Kevin Mills; Ashok Vellodi; Peter Morris; Donald Cooper; Michael Morris; Elisabeth Young; Bryan Winchester
Monitoring the clinical and biochemical response to enzyme replacement therapy in three children with Fabry disease.
European journal of pediatrics 2004;163(10):595-603.
2004: Els Schollen; Christian G Frank; Liesbeth Keldermans; R Reyntjens; Claudia E Grubenmann; Peter T Clayton; Bryan Winchester; Jan A M Smeitink; Ron A Wevers; Markus Aebi; Thierry Hennet; Gert Matthijs
Clinical and molecular features of three patients with congenital disorders of glycosylation type Ih (CDG-Ih) (ALG8 deficiency).
Journal of medical genetics 2004;41(7):550-6.
2004: Nicole Muschol; Stephan Storch; Diana Ballhausen; Clare E Beesley; Jan-Christoph Westermann; Andreas Gal; Kurt Ullrich; John J Hopwood; Bryan Winchester; Thomas Braulke
Transport, enzymatic activity, and stability of mutant sulfamidase (SGSH) identified in patients with mucopolysaccharidosis type III A.
Human mutation 2004;23(6):559-66.
2004: Clare E Beesley; Marina Moraitou; Bryan Winchester; K Schulpis; Evagelia Dimitriou; Helen Michelakakis
Sanfilippo B syndrome: molecular defects in Greek patients.
Clinical genetics 2004;65(2):143-9.
2003: Clare E Beesley; Derek Burke; Marie Jackson; Ashok Vellodi; Bryan Winchester; EP Young
Sanfilippo syndrome type D: identification of the first mutation in the N-acetylglucosamine-6-sulphatase gene.
Journal of medical genetics 2003;40(3):192-4.
2003: Kevin Mills; Philippa B Mills; Peter T Clayton; Nasi Mian; Andrew W Johnson; Bryan Winchester
The underglycosylation of plasma alpha 1-antitrypsin in congenital disorders of glycosylation type I is not random.
Glycobiology 2003;13(2):73-85.
2003: Philippa B Mills; Kevin Mills; Nasi Mian; Bryan Winchester; Peter T Clayton
Mass spectrometric analysis of glycans in elucidating the pathogenesis of CDG type IIx .
Journal of inherited metabolic disease 2003;26(2-3):119-34.
2003: Ursula Matte; Gouri Yogalingam; Doug Brooks; Sandra Leistner; Ida Schwartz; Luciane Lima; Denise Y J Norato; Jaime M Brum; Clare E Beesley; Bryan Winchester; Roberto Giugliani; John J Hopwood
Identification and characterization of 13 new mutations in mucopolysaccharidosis type I patients.
Molecular genetics and metabolism 2003;78(1):37-43.
2002: Kevin Mills; Andrew Johnson; Bryan Winchester
Synthesis of novel internal standards for the quantitative determination of plasma ceramide trihexoside in Fabry disease by tandem mass spectrometry.
FEBS letters 2002;515(1-3):171-6.
2001: Catharina Whybra; Christoph Kampmann; I Willers; J Davies; Bryan Winchester; Jörg Kriegsmann; K Brühl; Andreas Gal; S Bunge; M Beck
Anderson-Fabry disease: clinical manifestations of disease in female heterozygotes.
Journal of inherited metabolic disease 2001;24(7):715-24.
2001: Clare E Beesley; C A Meaney; G Greenland; V Adams; Ashok Vellodi; EP Young; Bryan Winchester
Mutational analysis of 85 mucopolysaccharidosis type I families: frequency of known mutations, identification of 17 novel mutations and in vitro expression of missense mutations.
Human genetics 2001;109(5):503-11.
2001: Kevin Mills; Philippa B Mills; Peter T Clayton; Andrew W Johnson; David Whitehouse; Bryan Winchester
Identification of alpha(1)-antitrypsin variants in plasma with the use of proteomic technology.
Clinical chemistry 2001;47(11):2012-22.
2001: Philippa Mills; Kevin Mills; Peter Clayton; A Johnson; David Whitehouse; Bryan Winchester
Congenital disorders of glycosylation type I leads to altered processing of N-linked glycans, as well as underglycosylation.
The Biochemical journal 2001;359(Pt 2):249-54.
2001: Chris Hendriksz; P McClean; M J Henderson; D G Keir; Viki Worthington; F Imtiaz; Els Schollen; Gert Matthijs; Bryan Winchester
Successful treatment of carbohydrate deficient glycoprotein syndrome type 1b with oral mannose.
Archives of disease in childhood 2001;85(4):339-40.
2001: E J Estruch; Stephen Hart; Christine Kinnon; Bryan Winchester
Non-viral, integrin-mediated gene transfer into fibroblasts from patients with lysosomal storage diseases.
The journal of gene medicine 2001;3(5):488-97.
2001: Philippa B Mills; Kevin Mills; Andrew W Johnson; Peter T Clayton; Bryan Winchester
Analysis by matrix assisted laser desorption/ionisation-time of flight mass spectrometry of the post-translational modifications of alpha 1-antitrypsin isoforms separated by two-dimensional polyacrylamide gel electrophoresis.
Proteomics 2001;1(6):778-86.
2001: Bryan Winchester
Are there useful biochemical markers of disease activity in lysosomal storage diseases?
Journal of inherited metabolic disease 2001;24 Suppl 2():52-6; discussion 45-6.
2001: EP Young; Viki Worthington; Marie Jackson; Bryan Winchester
Pre- and postnatal diagnosis of patients with CLN1 and CLN2 by assay of palmitoyl-protein thioesterase and tripeptidyl-peptidase I activities.
European journal of paediatric neurology : EJPN : official journal of the European Paediatric Neurology Society 2001;5 Suppl A():193-6.
2001: Bryan Winchester
Lysosomal membrane proteins.
European journal of paediatric neurology : EJPN : official journal of the European Paediatric Neurology Society 2001;5 Suppl A():11-9.
2000: Vibeke Westphal; Simon H Murch; S Kim; Geetha Srikrishna; Bryan Winchester; Richard Day; Hudson H Freeze
Reduced heparan sulfate accumulation in enterocytes contributes to protein-losing enteropathy in a congenital disorder of glycosylation.
The American journal of pathology 2000;157(6):1917-25.
2000: Gert Matthijs; Els Schollen; Cecilia Bjursell; Anna Erlandson; Hudson H Freeze; F Imtiaz; Susanne Kjaergaard; Tommy Martinsson; Marianne Schwartz; Nathalie Seta; Sandrine Vuillaumier-Barrot; Vibeke Westphal; Bryan Winchester
Mutations in PMM2 that cause congenital disorders of glycosylation, type Ia (CDG-Ia).
Human mutation 2000;16(5):386-94.
2000: P Whitfield; A W Johnson; K A Dunn; A J Delauche; Bryan Winchester; R J Franklin
GM1-gangliosidosis in a cross-bred dog confirmed by detection of GM1-ganglioside using electrospray ionisation-tandem mass spectrometry.
Acta neuropathologica 2000;100(4):409-14.
2000: Clare E Beesley; EP Young; Ashok Vellodi; Bryan Winchester
Mutational analysis of Sanfilippo syndrome type A (MPS IIIA): identification of 13 novel mutations.
Journal of medical genetics 2000;37(9):704-7.
2000: Els Schollen; Lambertus Dorland; Tom J de Koning; Otto P van Diggelen; Jan G M Huijmans; T Marquardt; D Babovic-Vuksanovic; M Patterson; F Imtiaz; Bryan Winchester; Maciej Adamowicz; Ewa Pronicka; Hudson H Freeze; Gert Matthijs
Genomic organization of the human phosphomannose isomerase (MPI) gene and mutation analysis in patients with congenital disorders of glycosylation type Ib (CDG-Ib).
Human mutation 2000;16(3):247-52.
2000: EP Young; Bryan Winchester; W Peter Logan; Ruth B Wheeler; BD Lake
Exclusion of late infantile neuronal ceroid lipofuscinosis (LINCL) in a fetus by assay of tripeptidyl peptidase I in chorionic villi.
Prenatal diagnosis 2000;20(4):337-9.
2000: F Imtiaz; Viki Worthington; M Champion; Clare E Beesley; J Charlwood; Peter Clayton; Geoffrey Keir; Nasi Mian; Bryan Winchester
Genotypes and phenotypes of patients in the UK with carbohydrate-deficient glycoprotein syndrome type 1.
Journal of inherited metabolic disease 2000;23(2):162-74.
2000: Bryan Winchester; Ashok Vellodi; Elisabeth Young
The molecular basis of lysosomal storage diseases and their treatment.
Biochemical Society transactions 2000;28(2):150-4.
1999: Markus Aebi; ari Helenius; B Schenk; R Barone; A Fiumara; Eric G Berger; Thierry Hennet; T Imbach; A Stutz; Cecilia Bjursell; A Uller; Jan Wahlström; Paz Briones; E Cardo; Peter Clayton; Bryan Winchester; V Cormier-Dalre; Pascale de Lonlay; Maryvonne Cuer; Thierry Dupré; Nathalie Seta; Tom J de Koning; Lambertus Dorland; F de Loos; L Kupers
Carbohydrate-deficient glycoprotein syndromes become congenital disorders of glycosylation: an updated nomenclature for CDG. First International Workshop on CDGS.
Glycoconjugate journal 1999;16(11):669-71.
1999: Bryan Winchester
Outlook for screening for sphingolipidoses.
Lancet 1999;354(9182):879-80.
1999: Ashok Vellodi; E Young; A Cooper; V Lidchi; Bryan Winchester; James Wraith
Long-term follow-up following bone marrow transplantation for Hunter disease.
Journal of inherited metabolic disease 1999;22(5):638-48.
1999: Geoffrey Keir; Bryan Winchester; Peter Clayton
Carbohydrate-deficient glycoprotein syndromes: inborn errors of protein glycosylation.
Annals of clinical biochemistry 1999;36 ( Pt 1)():20-36.
1998: O Diettrich; Kevin Mills; Andrew W Johnson; A Hasilik; Bryan Winchester
Application of magnetic chromatography to the isolation of lysosomes from fibroblasts of patients with lysosomal storage disorders.
FEBS letters 1998;441(3):369-72.
1998: Clare E Beesley; EP Young; Ashok Vellodi; Bryan Winchester
Identification of 12 novel mutations in the alpha-N-acetylglucosaminidase gene in 14 patients with Sanfilippo syndrome type B (mucopolysaccharidosis type IIIB).
Journal of medical genetics 1998;35(11):910-4.
1998: J Charlwood; Peter Clayton; Geoffrey Keir; Nasi Mian; E Young; Bryan Winchester
Prenatal diagnosis of the carbohydrate-deficient glycoprotein syndrome type 1A (CDG1A) by a combination of enzymology and genetic linkage analysis after amniocentesis or chorionic villus sampling.
Prenatal diagnosis 1998;18(7):693-9.
1998: J Charlwood; Peter Clayton; Geoffrey Keir; Nasi Mian; Bryan Winchester
Defective galactosylation of serum transferrin in galactosemia.
Glycobiology 1998;8(4):351-7.
1998: BD Lake; EP Young; Bryan Winchester
Prenatal diagnosis of lysosomal storage diseases.
Brain pathology (Zurich, Switzerland) 1998;8(1):133-49.
1997: J Charlwood; Peter Clayton; A Johnson; Geoffrey Keir; Nasi Mian; Bryan Winchester
A case of the carbohydrate-deficient glycoprotein syndrome type 1 (CDGS type 1) with normal phosphomannomutase activity.
Journal of inherited metabolic disease 1997;20(6):817-26.
1997: E Young; C Chatterton; Ashok Vellodi; Bryan Winchester
Plasma chitotriosidase activity in Gaucher disease patients who have been treated either by bone marrow transplantation or by enzyme replacement therapy with alglucerase.
Journal of inherited metabolic disease 1997;20(4):595-602.
1997: Ashok Vellodi; EP Young; A Cooper; James Wraith; Bryan Winchester; C Meaney; Uma Ramaswami; Andrew M Will
Bone marrow transplantation for mucopolysaccharidosis type I: experience of two British centres.
Archives of disease in childhood 1997;76(2):92-9.
1997: H Cragg; M Williamson; E Young; J O'Brien; J Alhadeff; S Fang-Kircher; Eduard Paschke; Bryan Winchester
Fucosidosis: genetic and biochemical analysis of eight cases.
Journal of medical genetics 1997;34(2):105-10.
1996: Oleg Iourin; Taj S Mattu; Nasi Mian; Geoffrey Keir; Bryan Winchester; Raymond A Dwek; Pauline M Rudd
The identification of abnormal glycoforms of serum transferrin in carbohydrate deficient glycoprotein syndrome type I by capillary zone electrophoresis.
Glycoconjugate journal 1996;13(6):1031-42.
1996: J P Davies; C M Eng; J A Hill; Sue Malcolm; K MacDermot; Bryan Winchester; R J Desnick
Fabry disease: fourteen alpha-galactosidase A mutations in unrelated families from the United Kingdom and other European countries.
European journal of human genetics : EJHG 1996;4(4):219-24.
1996: S L Goldenfum; E Young; H Michelakakis; S Tsagarakis; Bryan Winchester
Mutation analysis in 20 patients with Hunter disease.
Human mutation 1996;7(1):76-8.
1995: Bryan Winchester; Peter Clayton; Nasi Mian; E di-Tomaso; A Dell; A Reason; Geoffrey Keir
The carbohydrate-deficient glycoprotein syndrome: an experiment of nature in glycosylation.
Biochemical Society transactions 1995;23(1):185-8.
1995: S Leistner; E Young; C Meaney; Bryan Winchester
Pseudodeficiency of arylsulphatase A: strategy for clarification of genotype in families of subjects with low ASA activity and neurological symptoms.
Journal of inherited metabolic disease 1995;18(6):710-6.
1995: Ashok Vellodi; H Cragg; Bryan Winchester; E Young; J Young; C J Downie; R D Hoare; R Stocks; G K Banerjee
Allogeneic bone marrow transplantation for fucosidosis.
Bone marrow transplantation 1995;15(1):153-8.
1994: P F Daniel; Bryan Winchester; C D Warren
Mammalian alpha-mannosidases--multiple forms but a common purpose?
Glycobiology 1994;4(5):551-66.
1994: Joël Zlotogora; Y Furman-Shaharabani; S Goldenfum; Bryan Winchester; K von Figura; V Gieselmann
Arylsulfatase A pseudodeficiency: a common polymorphism which is associated with a unique haplotype.
American journal of medical genetics 1994;52(2):146-50.
1994: H Cragg; Bryan Winchester; H C Seo; J O'Brien; D Swallow
Molecular basis of the common electrophoretic polymorphism (Fu1/Fu2) in human alpha-L-fucosidase.
Journal of medical genetics 1994;31(8):659-60.
1993: J P Davies; Bryan Winchester; Sue Malcolm
Sequence variations in the first exon of alpha-galactosidase A.
Journal of medical genetics 1993;30(8):658-63.
1993: J P Davies; Bryan Winchester; Sue Malcolm
Mutation analysis in patients with the typical form of Anderson-Fabry disease.
Human molecular genetics 1993;2(7):1051-3.
1993: S Goldenfum; Sue Malcolm; Bryan Winchester
An 8-bp deletion in exon B of the iduronate-2-sulphate sulphatase gene in a case of Hunter disease.
Human molecular genetics 1993;2(7):1063-5.
1993: Peter Clayton; Bryan Winchester; E Di Tomaso; E Young; Geoffrey Keir; C Rodeck
Carbohydrate-deficient glycoprotein syndrome: normal glycosylation in the fetus.
Lancet 1993;341(8850):956.
1993: Bryan Winchester; S al Daher; N C Carpenter; I Cenci di Bello; S S Choi; A J Fairbanks; George W J Fleet
The structural basis of the inhibition of human alpha-mannosidases by azafuranose analogues of mannose.
The Biochemical journal 1993;290 ( Pt 3)():743-9.
1993: M Williamson; H Cragg; J Grant; K Kretz; J O'Brien; P J Willems; E Young; Bryan Winchester
A 5' splice site mutation in fucosidosis.
Journal of medical genetics 1993;30(3):218-23.
1993: S Goldenfum; Sue Malcolm; E Young; Bryan Winchester
The molecular detection of the pseudodeficiency allele for arylsulphatase A in patients with neurological symptoms and low arylsulphatase A activity.
Journal of inherited metabolic disease 1993;16(6):1048-9.
1992: Bryan Winchester; E Young; S Geddes; S Genet; J Hurst; H Middleton-Price; N Williams; M Webb; A Habel; Sue Malcolm
Female twin with Hunter disease due to nonrandom inactivation of the X-chromosome: a consequence of twinning.
American journal of medical genetics 1992;44(6):834-8.
1992: R De Gasperi; S al Daher; Bryan Winchester; C D Warren
Substrate specificity of the bovine and feline neutral alpha-mannosidases.
The Biochemical journal 1992;286 ( Pt 1)():55-63.
1992: S al Daher; R De Gasperi; P Daniel; S Hirani; C Warren; Bryan Winchester
Substrate specificity of human liver neutral alpha-mannosidase.
The Biochemical journal 1992;286 ( Pt 1)():47-53.
1992: P F Daniel; J E Evans; R De Gasperi; Bryan Winchester; C D Warren
A human lysosomal alpha(1----6)-mannosidase active on the branched trimannosyl core of complex glycans.
Glycobiology 1992;2(4):327-36.
1992: Bryan Winchester; G W Fleet
Amino-sugar glycosidase inhibitors: versatile tools for glycobiologists.
Glycobiology 1992;2(3):199-210.
1992: Peter T Clayton; Bryan Winchester; Geoffrey Keir
Hypertrophic obstructive cardiomyopathy in a neonate with the carbohydrate-deficient glycoprotein syndrome.
Journal of inherited metabolic disease 1992;15(6):857-61.
1991: R DeGasperi; S al Daher; P F Daniel; Bryan Winchester; R W Jeanloz; C D Warren
The substrate specificity of bovine and feline lysosomal alpha-D-mannosidases in relation to alpha-mannosidosis.
The Journal of biological chemistry 1991;266(25):16556-63.
1991: S P Horslen; Peter T Clayton; B N Harding; N A Hall; Geoffrey Keir; Bryan Winchester
Olivopontocerebellar atrophy of neonatal onset and disialotransferrin developmental deficiency syndrome.
Archives of disease in childhood 1991;66(9):1027-32.
1991: S al Daher; R de Gasperi; P Daniel; N Hall; C D Warren; Bryan Winchester
The substrate-specificity of human lysosomal alpha-D-mannosidase in relation to genetic alpha-mannosidosis.
The Biochemical journal 1991;277 ( Pt 3)():743-51.
1990: George W J Fleet; N G Ramsden; Robert J Nash; L E Fellows; Gary S Jacob; R J Molyneux; I C di Bello; Bryan Winchester
Synthesis of the enantiomers of 6-epicastanospermine and 1,6-diepicastanospermine from D- and L-gulonolactone.
Carbohydrate research 1990;205():269-82.
1990: W F Collin; George W J Fleet; M Haraldsson; I Cenci di Bello; Bryan Winchester
Effect on human liver glycosidases and short syntheses of 1 alpha,2 alpha,6 alpha,7 alpha,7a beta-1,2,6,7-tetrahydroxypyrrolizidine from D-glycero-D-gulo-heptono-1,4-lactone.
Carbohydrate research 1990;202():105-16.
1990: Bryan Winchester; I Cenci di Bello; A C Richardson; Robert J Nash; L E Fellows; N G Ramsden; George W J Fleet
The structural basis of the inhibition of human glycosidases by castanospermine analogues.
The Biochemical journal 1990;269(1):227-31.
1990: Bryan Winchester
Prenatal diagnosis of enzyme defects.
Archives of disease in childhood 1990;65(1 Spec No):59-67.
1990: George W J Fleet; L E Fellows; Bryan Winchester
Plagiarizing plants: amino sugars as a class of glycosidase inhibitors.
Ciba Foundation symposium 1990;154():112-22; discussion 122-5.
1990: Bryan Winchester; C Barker; S Baines; Gary S Jacob; S K Namgoong; George W J Fleet
Inhibition of alpha-L-fucosidase by derivatives of deoxyfuconojirimycin and deoxymannojirimycin.
The Biochemical journal 1990;265(1):277-82.
1989: R Desgasperi; S al Daher; N Hall; Bryan Winchester; C D Warren
Specificity of lysosomal alpha-mannosidase for natural substrates.
Biochemical Society transactions 1989;17(6):1036-7.
1989: I Cenci di Bello; George W J Fleet; S K Namgoong; K Tadano; Bryan Winchester
Structure-activity relationship of swainsonine. Inhibition of human alpha-mannosidases by swainsonine analogues.
The Biochemical journal 1989;259(3):855-61.
1989: S al Daher; George W J Fleet; S K Namgoong; Bryan Winchester
Change in specificity of glycosidase inhibition by N-alkylation of amino sugars.
The Biochemical journal 1989;258(2):613-5.
1988: C Barker; A Dell; M Rogers; J A Alhadeff; Bryan Winchester
Canine alpha-L-fucosidase in relation to the enzymic defect and storage products in canine fucosidosis.
The Biochemical journal 1988;254(3):861-8.
1985: S Hirani; Bryan Winchester
Changes in human plasma alpha-D-mannosidase activity during pregnancy.
Clinica chimica acta; international journal of clinical chemistry 1985;152(1-2):71-7.
1984: I Cenci di Bello; P Dorling; L Fellows; Bryan Winchester
Specific inhibition of human beta-D-glucuronidase and alpha-L-iduronidase by a trihydroxy pipecolic acid of plant origin.
FEBS letters 1984;176(1):61-4.
1983: I Cenci di Bello; P Dorling; Bryan Winchester
The storage products in genetic and swainsonine-induced human mannosidosis.
The Biochemical journal 1983;215(3):693-6.
1983: K Chotai; C Jennings; Bryan Winchester; P Dorling
The uptake of swainsonine, a specific inhibitor of alpha-D-mannosidase, into normal human fibroblasts in culture.
Journal of cellular biochemistry 1983;21(2):107-17.
1980: S Hirani; Bryan Winchester
Plasma alpha-D-mannosidase in mucolipidosis II and mucolipidosis III.
Clinica chimica acta; international journal of clinical chemistry 1980;101(2-3):251-6.