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Michael Knowles

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Michael Knowles; Margaret W Leigh; Niki Tomas Loges; Adriana Lori; Susan L Minnix; Heike Olbrich; Kenneth N Olivier; Heymut Omran; Margaret Rosenfeld; Scott D Sagel; Miriam Schmidts; Claudius Werner; Maimoona A Zariwala; Michael C Armstrong; Anita Becker-Heck; Kimberlie A Burns; Johnny L Carson; Stephanie D Davis; Sharon D Dell; Thomas Ferkol; Milan J Hazucha
Mutations of DNAH11 in patients with primary ciliary dyskinesia with normal ciliary ultrastructure.
Chelsea Taylor; Aaron D Webel; Fred A Wright; Julian Zielenski; Yves Berthiaume; SCOTT BLACKMAN; Michael MICHAEL Collaco; Clayton W Commander; Garry R Cutting; Ruslan Dorfman; Mitchell L Drumm; Peter Roy Durie; Michael Knowles; Weili Li; Kathleen Naughton; Rhonda G Pace; Peter Paré; Andrew Sandford; Jaclyn R Stonebraker; Lisa J Strug; Mary Corey
A novel lung disease phenotype adjusted for mortality attrition for cystic fibrosis genetic modifier studies.
William T Harris; Michael Knowles; Marianne S Muhlebach; John P Clancy; Robert A Oster; Terry L Noah
Plasma TGF-β₁ in pediatric cystic fibrosis: potential biomarker of lung disease and response to therapy.

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2012: Michael Knowles; Margaret W Leigh; Niki Tomas Loges; Adriana Lori; Susan L Minnix; Heike Olbrich; Kenneth N Olivier; Heymut Omran; Margaret Rosenfeld; Scott D Sagel; Miriam Schmidts; Claudius Werner; Maimoona A Zariwala; Michael C Armstrong; Anita Becker-Heck; Kimberlie A Burns; Johnny L Carson; Stephanie D Davis; Sharon D Dell; Thomas Ferkol; Milan J Hazucha
Mutations of DNAH11 in patients with primary ciliary dyskinesia with normal ciliary ultrastructure.
Thorax 2012;67(5):433-41.
2011: Chelsea Taylor; Aaron D Webel; Fred A Wright; Julian Zielenski; Yves Berthiaume; SCOTT BLACKMAN; Michael MICHAEL Collaco; Clayton W Commander; Garry R Cutting; Ruslan Dorfman; Mitchell L Drumm; Peter Roy Durie; Michael Knowles; Weili Li; Kathleen Naughton; Rhonda G Pace; Peter Paré; Andrew Sandford; Jaclyn R Stonebraker; Lisa J Strug; Mary Corey
A novel lung disease phenotype adjusted for mortality attrition for cystic fibrosis genetic modifier studies.
Pediatric pulmonology 2011;46(9):857-69.
2011: William T Harris; Michael Knowles; Marianne S Muhlebach; John P Clancy; Robert A Oster; Terry L Noah
Plasma TGF-β₁ in pediatric cystic fibrosis: potential biomarker of lung disease and response to therapy.
Pediatric pulmonology 2011;46(7):688-95.
2011: Jonathan S Berg; James P Evans; Margaret W Leigh; Heymut Omran; Chris Bizon; Ketan Mane; Michael Knowles; Karen E Weck; Maimoona A Zariwala
Next generation massively parallel sequencing of targeted exomes to identify genetic mutations in primary ciliary dyskinesia: implications for application to clinical testing.
Genetics in medicine : official journal of the American College of Medical Genetics 2011;13(3):218-29.
2011: W Li; Lei Sun; Mary Corey; F Zou; S Lee; A L Cojocaru; Carol L Freund-Taylor; SCOTT BLACKMAN; A Stephenson; A J Sandford; R Dorfman; Mitchell L Drumm; Garry R Cutting; Michael Knowles; Peter Roy Durie; F A Wright; Lisa J Strug
Understanding the population structure of North American patients with cystic fibrosis.
Clinical genetics 2011;79(2):136-46.
2010: Rebecca Darrah; Edward McKone; Clare O'Connor; Christine Rodgers; Alan Genatossio; Sharon McNamara; Ronald Gibson; J Stuart Elborn; Madeleine Ennis; Charles G Gallagher; Noor Kalsheker; Moira Aitken; Dawn Wiese; John Dunn; Paul Smith; Rhonda Pace; Douglas Londono; Katrina Goddard; Michael Knowles; Mitchell L Drumm
EDNRA variants associate with smooth muscle mRNA levels, cell proliferation rates, and cystic fibrosis pulmonary disease severity.
Physiological genomics 2010;41(1):71-7.
2009: Niki Tomas Loges; Heike Olbrich; Anita Becker-Heck; Karsten Häffner; Angelina Heer; Christina Reinhard; Miriam Schmidts; Andreas Kispert; Maimoona A Zariwala; Margaret W Leigh; Michael Knowles; Hanswalter Zentgraf; Horst Seithe; Gudrun Nürnberg; Peter Nürnberg; Richard Reinhardt; Heymut Omran
Deletions and point mutations of LRRC50 cause primary ciliary dyskinesia due to dynein arm defects.
American journal of human genetics 2009;85(6):883-9.
2009: William T Harris; Marianne S Muhlebach; Robert A Oster; Michael Knowles; Terry L Noah
Transforming growth factor-beta(1) in bronchoalveolar lavage fluid from children with cystic fibrosis.
Pediatric pulmonology 2009;44(11):1057-64.
2009: Jaclyn R Bartlett; Kenneth Friedman; Simon C Ling; Rhonda G Pace; Scott C Bell; Billy Bourke; Giuseppe Castaldo; Carlo Castellani; Marco Cipolli; Carla Colombo; John L Colombo; Dominique Debray; Adriana Fernandez; Florence Lacaille; Milan Macek Jr.; Marion Rowland; Francesco Salvatore; Christopher J Taylor; Claire Wainwright; Michael Wilschanski; Dana Zemková; William B Hannah; M James Phillips; Mary Corey; Julian Zielenski; Ruslan Dorfman; Yunfei Wang; Fei Zou; Lawrence M Silverman; Mitchell L Drumm; Fred A Wright; Ethan M Lange; Peter Roy Durie; Michael Knowles
Genetic modifiers of liver disease in cystic fibrosis.
JAMA : the journal of the American Medical Association 2009;302(10):1076-83.
2009: SCOTT BLACKMAN; STEPHANIE HSU; S E Ritter; K M Naughton; Fred A Wright; M L Drumm; Michael Knowles; Garry R Cutting
A susceptibility gene for type 2 diabetes confers substantial risk for diabetes complicating cystic fibrosis.
Diabetologia 2009;52(9):1858-65.
2009: Margaret W Leigh; Jessica E Pittman; Johnny L Carson; Thomas W Ferkol; Sharon D Dell; Stephanie D Davis; Michael Knowles; Maimoona A Zariwala
Clinical and genetic aspects of primary ciliary dyskinesia/Kartagener syndrome.
Genetics in medicine : official journal of the American College of Medical Genetics 2009;11(7):473-87.
2009: Hara Levy; Amy Murphy; Fei Zou; Craig Gerard; Barbara J Klanderman; Brooke Schuemann; Ross Lazarus; K Christopher García; Juan C Celedón; Mitch Drumm; Mary Dahmer; Michael Quasney; Kaitlyn Schneck; Melissa Reske; Michael Knowles; Gerald B Pier; Christoph Lange; Scott Weiss
IL1B polymorphisms modulate cystic fibrosis lung disease.
Pediatric pulmonology 2009;44(6):580-93.
2009: Margaret W Leigh; Maimoona A Zariwala; Michael Knowles
Primary ciliary dyskinesia: improving the diagnostic approach.
Current opinion in pediatrics 2009;21(3):320-5.
2009: YuanYuan Gu; Isaac T W Harley; Lindsay B Henderson; Bruce Aronow; Ilja Vietor; Lukas A Huber; John B Harley; Jeffrey R Kilpatrick; Carl D Langefeld; Adrienne H Williams; Anil G Jegga; Jing Chen; MARSHA WILLS-KARP; S Hasan Arshad; Susan L Ewart; Chloe L Thio; Leah M Flick; Marie-Dominique Filippi; H Leighton Grimes; Mitchell L Drumm; Garry R Cutting; Michael Knowles; Christopher L Karp
Identification of IFRD1 as a modifier gene for cystic fibrosis lung disease.
Nature 2009;458(7241):1039-42.
2009: Jennifer L Taylor-Cousar; Maimoona A Zariwala; Lauranell H Burch; Rhonda G Pace; Mitchell L Drumm; Hollin Calloway; Haiying Fan; Brent W Weston; Fred A Wright; Michael Knowles
Histo-blood group gene polymorphisms as potential genetic modifiers of infection and cystic fibrosis lung disease severity.
PloS one 2009;4(1):e4270.
2008: A D Hillian; D Londono; John M Dunn; Katrina Goddard; R G Pace; Michael Knowles; M L Drumm
Modulation of cystic fibrosis lung disease by variants in interleukin-8.
Genes and immunity 2008;9(6):501-8.
2008: C Castellani; H Cuppens; Milan Macek Jr.; J J Cassiman; E Kerem; Peter Roy Durie; E Tullis; B M Assael; C Bombieri; A Brown; T Casals; M Claustres; Garry R Cutting; E Dequeker; J Dodge; I Doull; P Farrell; C Ferec; E Girodon; M Johannesson; B Kerem; Michael Knowles; A Munck; P F Pignatti; Dragica Radojkovic; P Rizzotti; M Schwarz; M Stuhrmann; Maria Tzetis; J Zielenski; J S Elborn
Consensus on the use and interpretation of cystic fibrosis mutation analysis in clinical practice.
Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society 2008;7(3):179-96.
2007: Zhibing Zhang; Maimoona A Zariwala; Maha M Mahadevan; Pedro Caballero-Campo; Xuening Shen; Estelle Escudier; Bénédicte Duriez; Anne-Marie Bridoux; Margaret W Leigh; George Gerton; Marcus Kennedy; Serge Amselem; Michael Knowles; Jerome F Strauss
A heterozygous mutation disrupting the SPAG16 gene results in biochemical instability of central apparatus components of the human sperm axoneme.
Biology of reproduction 2007;77(5):864-71.
2007: Ali Mencin; Ekihiro Seki; Yosuke Osawa; Yuzo Kodama; Samuele De Minicis; Michael Knowles; David A Brenner
Alpha-1 antitrypsin Z protein (PiZ) increases hepatic fibrosis in a murine model of cholestasis.
Hepatology (Baltimore, Md.) 2007;46(5):1443-52.
2007: Marcus Peter Kennedy; Peadar G Noone; Michael Knowles
[Airway calcium deposition and broncholithiasis in disorders of mucociliary clearance].
Archivos de bronconeumología 2007;43(8):474.
2007: John P Clancy; Steven M Rowe; Zsuzsa Bebok; Moira L Aitken; Ron Gibson; Pamela L Zeitlin; Pierre Berclaz; Richard Moss; Michael Knowles; Robert A Oster; Nicole Mayer-Hamblett; Bonnie W Ramsey
No detectable improvements in cystic fibrosis transmembrane conductance regulator by nasal aminoglycosides in patients with cystic fibrosis with stop mutations.
American journal of respiratory cell and molecular biology 2007;37(1):57-66.
2007: Marcus P Kennedy; Raymond D Coakley; Scott H Donaldson; Robert M Aris; Kathy Hohneker; Joel P Wedd; Michael Knowles; Peter H Gilligan; James R Yankaskas
Burkholderia gladioli: five year experience in a cystic fibrosis and lung transplantation center.
Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society 2007;6(4):267-73.
2007: Marcus P Kennedy; Heymut Omran; Margaret W Leigh; Sharon Dell; Lucy Morgan; Paul L Molina; Blair Robinson; Susan L Minnix; Heike Olbrich; Thomas Severin; Peter Ahrens; Lars Lange; Hilda N Morillas; Peadar G Noone; Maimoona A Zariwala; Michael Knowles
Congenital heart disease and other heterotaxic defects in a large cohort of patients with primary ciliary dyskinesia.
Circulation 2007;115(22):2814-21.
2007: Marcus P Kennedy; Peadar G Noone; Margaret W Leigh; Maimoona A Zariwala; Susan L Minnix; Michael Knowles; Paul L Molina
High-resolution CT of patients with primary ciliary dyskinesia.
AJR. American journal of roentgenology 2007;188(5):1232-8.
2007: Hilda N Morillas; Maimoona A Zariwala; Michael Knowles
Genetic causes of bronchiectasis: primary ciliary dyskinesia.
Respiration; international review of thoracic diseases 2007;74(3):252-63.
2007: Maimoona A Zariwala; Michael Knowles; Heymut Omran
Genetic defects in ciliary structure and function.
Annual review of physiology 2007;69():423-50.
2007: Marcus P Kennedy; Peadar G Noone; Johnny L Carson; Paul L Molina; Andrew Ghio; Maimoona A Zariwala; Susan L Minnix; Michael Knowles
Calcium stone lithoptysis in primary ciliary dyskinesia.
Respiratory medicine 2007;101(1):76-83.
2006: Michael Knowles
Gene modifiers of lung disease.
Current opinion in pulmonary medicine 2006;12(6):416-21.
2006: Maimoona A Zariwala; Margaret W Leigh; Franck Ceppa; Marcus P Kennedy; Peadar G Noone; Johnny L Carson; Milan J Hazucha; Adriana Lori; Judit Horvath; Heike Olbrich; Niki Tomas Loges; Anne-Marie Bridoux; Gaëlle Pennarun; Bénédicte Duriez; Estelle Escudier; Hannah M Mitchison; Rahul Chodhari; Eddie M K Chung; Lucy C Morgan; Robbert U de Iongh; Jonathan Rutland; Ugo Pradal; Heymut Omran; Serge Amselem; Michael Knowles
Mutations of DNAI1 in primary ciliary dyskinesia: evidence of founder effect in a common mutation.
American journal of respiratory and critical care medicine 2006;174(8):858-66.
2006: Mark Schluchter; Michael W Konstan; Mitchell L Drumm; James R Yankaskas; Michael Knowles
Classifying severity of cystic fibrosis lung disease using longitudinal pulmonary function data.
American journal of respiratory and critical care medicine 2006;174(7):780-6.
2006: Nada Hornef; Heike Olbrich; Judit Horvath; Maimoona A Zariwala; Manfred Fliegauf; Niki Tomas Loges; Johannes H Wildhaber; Peadar G Noone; Marcus Kennedy; Stylianos E Antonarakis; Jean-Louis Blouin; Lucia Bartoloni; Thomas Nüsslein; Peter Ahrens; Matthias Griese; Heiner Kuhl; Ralf Sudbrak; Michael Knowles; Richard Reinhardt; Heymut Omran
DNAH5 mutations are a common cause of primary ciliary dyskinesia with outer dynein arm defects.
American journal of respiratory and critical care medicine 2006;174(2):120-6.
2006: Barbara R Grubb; Sherif E Gabriel; April Mengos; Martina Gentzsch; Scott H Randell; Anna van Heeckeren; Michael Knowles; Mitchell L Drumm; John R Riordan; Richard C Boucher
SERCA pump inhibitors do not correct biosynthetic arrest of deltaF508 CFTR in cystic fibrosis.
American journal of respiratory cell and molecular biology 2006;34(3):355-63.
2006: Scott H Donaldson; William D Bennett; Kirby L Zeman; Michael Knowles; Robert Tarran; Richard C Boucher
Mucus clearance and lung function in cystic fibrosis with hypertonic saline.
The New England journal of medicine 2006;354(3):241-50.
2005: Molly B Sheridan; Peying Fong; Joshua D Groman; Carol Conrad; Patrick A Flume; Ruben Diaz; Christopher Harris; Michael Knowles; Garry R Cutting
Mutations in the beta-subunit of the epithelial Na+ channel in patients with a cystic fibrosis-like syndrome.
Human molecular genetics 2005;14(22):3493-8.
2005: Mitchell L Drumm; Michael W Konstan; Mark Schluchter; Allison Handler; Rhonda Pace; Fei Zou; Maimoona A Zariwala; David Fargo; Airong Xu; John M Dunn; Rebecca J Darrah; Ruslan Dorfman; Andrew J Sandford; Mary Corey; Julian Zielenski; Peter Roy Durie; Katrina Goddard; James R Yankaskas; Fred A Wright; Michael Knowles
Genetic modifiers of lung disease in cystic fibrosis.
The New England journal of medicine 2005;353(14):1443-53.
2005: Kathryn Chmura; Edward D Chan; Peadar G Noone; Maimoona A Zariwala; Robert A Winn; Michael Knowles; Michael D Iseman; Edward M Gardner
A middle-aged woman with recurrent respiratory infections.
Respiration; international review of thoracic diseases 2005;72(4):427-30.
2005: W Edward Highsmith; Kenneth Friedman; L H Burch; A Spock; Lawrence M Silverman; Richard C Boucher; Michael Knowles
A CFTR mutation (D1152H) in a family with mild lung disease and normal sweat chlorides.
Clinical genetics 2005;68(1):88-90.
2005: Judit Horváth; Manfred Fliegauf; Heike Olbrich; Andreas Kispert; Stephen M King; Hannah M Mitchison; Maimoona A Zariwala; Michael Knowles; Ralf Sudbrak; György Fekete; Juergen Neesen; Richard Reinhardt; Heymut Omran
Identification and analysis of axonemal dynein light chain 1 in primary ciliary dyskinesia patients.
American journal of respiratory cell and molecular biology 2005;33(1):41-7.
2005: Manfred Fliegauf; Heike Olbrich; Judit Horvath; Johannes H Wildhaber; Maimoona A Zariwala; Marcus Kennedy; Michael Knowles; Heymut Omran
Mislocalization of DNAH5 and DNAH9 in respiratory cells from patients with primary ciliary dyskinesia.
American journal of respiratory and critical care medicine 2005;171(12):1343-9.
2004: Ronald J Pettis; Michael Knowles; Kenneth N Olivier; Masha Kazantseva; Anthony J Hickey
Ionic interaction of amiloride and uridine 5'-triphosphate in nebulizer solutions.
Journal of pharmaceutical sciences 2004;93(9):2399-406.
2004: Daniel Schüler; Isabelle Sermet-Gaudelus; Michael Wilschanski; Manfred Ballmann; Michèle Dechaux; Aleksander Edelman; Martin Hug; Teresinha Leal; Jean Lebacq; Patrick LEBECQUE; Gérard Lenoir; Frauke Stanke; Pierre Wallemacq; Burkhard Tümmler; Michael Knowles
Basic protocol for transepithelial nasal potential difference measurements.
Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society 2004;3 Suppl 2():151-5.
2004: Thomas A Standaert; Louis Boitano; Julia Emerson; Laura J H Milgram; Michael W Konstan; Janice Hunter; Pierre-Yves Berclaz; Lois Brass; Pamela L Zeitlin; Keith B Hammond; Zoe Davies; Carla Foy; Peadar G Noone; Michael Knowles
Standardized procedure for measurement of nasal potential difference: an outcome measure in multicenter cystic fibrosis clinical trials.
Pediatric pulmonology 2004;37(5):385-92.
2004: Maimoona A Zariwala; Wanda O Neal; Peadar G Noone; Margaret W Leigh; Michael Knowles; Lawrence E Ostrowski
Investigation of the possible role of a novel gene, DPCD, in primary ciliary dyskinesia.
American journal of respiratory cell and molecular biology 2004;30(4):428-34.
2004: Christie P Thomas; Jackie Zhou; Kang Z Liu; Verity E Mick; Eithne MacLaughlin; Michael Knowles
Gene symbol: SCNN1B. Disease: Pseudohypoaldosteronism, type 1.
Human genetics 2004;114(4):402.
2004: Peadar G Noone; Margaret W Leigh; Aruna Sannuti; Susan L Minnix; Johnny L Carson; Milan J Hazucha; Maimoona A Zariwala; Michael Knowles
Primary ciliary dyskinesia: diagnostic and phenotypic features.
American journal of respiratory and critical care medicine 2004;169(4):459-67.
2003: Michael P Boyle; Marie Diener-West; Laura J H Milgram; Michael Knowles; Carla Foy; Pamela L Zeitlin; Thomas A Standaert
A multicenter study of the effect of solution temperature on nasal potential difference measurements.
Chest 2003;124(2):482-9.
2003: Andreas Kispert; Marianne Petry; Heike Olbrich; Andreas Volz; Uwe-Peter Ketelsen; Judit Horvath; Rachid Melkaoui; Heymut Omran; Maimoona A Zariwala; Peadar G Noone; Michael Knowles
Genotype-phenotype correlations in PCD patients carrying DNAH5 mutations.
Thorax 2003;58(6):552-4.
2003: Kenneth N Olivier; David J Weber; Ji-Hyun Lee; Allison Handler; Gail Tudor; Paul L Molina; Joseph F Tomashefski; Michael Knowles
Nontuberculous mycobacteria. II: nested-cohort study of impact on cystic fibrosis lung disease.
American journal of respiratory and critical care medicine 2003;167(6):835-40.
2003: Kenneth N Olivier; David J Weber; Richard J Wallace; Ali R Faiz; Ji-Hyun Lee; Yansheng Zhang; Barbara A Brown-Elliot; Allison Handler; Rebecca W Wilson; Michael S Schechter; Lloyd J Edwards; Subha Chakraborti; Michael Knowles
Nontuberculous mycobacteria. I: multicenter prevalence study in cystic fibrosis.
American journal of respiratory and critical care medicine 2003;167(6):828-34.
2003: Namita Sood; William D Bennett; Kirby L Zeman; James Brown; Carla Foy; Richard C Boucher; Michael Knowles
Increasing concentration of inhaled saline with or without amiloride: effect on mucociliary clearance in normal subjects.
American journal of respiratory and critical care medicine 2003;167(2):158-63.
2002: David N Collier; Lisa Anderson; Susan L McKnight; Terry L Noah; Michael Knowles; Richard C Boucher; Ute E Schwab; Peter H Gilligan; Everett C Pesci
A bacterial cell to cell signal in the lungs of cystic fibrosis patients.
FEMS microbiology letters 2002;215(1):41-6.
2002: Elizabeth M Rohlfs; Zhaoqing Zhou; Elaine A Sugarman; Ruth A Heim; Rhonda G Pace; Michael Knowles; Lawrence M Silverman; Bernice A Allitto
The I148T CFTR allele occurs on multiple haplotypes: a complex allele is associated with cystic fibrosis.
Genetics in medicine : official journal of the American College of Medical Genetics 2002;4(5):319-23.
2002: Christie P Thomas; Jackie Zhou; Kang Z Liu; Verity E Mick; Eithne MacLaughlin; Michael Knowles
Systemic pseudohypoaldosteronism from deletion of the promoter region of the human Beta epithelial na(+) channel subunit.
American journal of respiratory cell and molecular biology 2002;27(3):314-9.
2002: Michael Knowles; Peter Roy Durie
What is cystic fibrosis?
The New England journal of medicine 2002;347(6):439-42.
2002: Peadar G Noone; Maimoona A Zariwala; Aruna Sannuti; Susan L Minnix; Margaret W Leigh; Johnny L Carson; Michael Knowles
Mutations in DNAI1 (IC78) cause primary ciliary dyskinesia.
Chest 2002;121(3 Suppl):97S.
2002: Michael Knowles; Richard C Boucher
Mucus clearance as a primary innate defense mechanism for mammalian airways.
The Journal of clinical investigation 2002;109(5):571-7.
2002: Heike Olbrich; Karsten Häffner; Andreas Kispert; Alexander Völkel; Andreas Volz; Gürsel Sasmaz; Richard Reinhardt; Steffen Hennig; Hans Lehrach; Nikolaus Konietzko; Maimoona A Zariwala; Peadar G Noone; Michael Knowles; Hannah M Mitchison; Maggie Meeks; Eddie M K Chung; Friedhelm Hildebrandt; Ralf Sudbrak; Heymut Omran
Mutations in DNAH5 cause primary ciliary dyskinesia and randomization of left-right asymmetry.
Nature genetics 2002;30(2):143-4.
2002: Ray A Caldwell; Barbara R Grubb; Robert Tarran; Richard C Boucher; Michael Knowles; Pierre M Barker
In vivo airway surface liquid Cl- analysis with solid-state electrodes.
The Journal of general physiology 2002;119(1):3-14.
2001: Peadar G Noone; Z Zhou; Lawrence M Silverman; Paul S Jowell; Michael Knowles; Jonathan A Cohn
Cystic fibrosis gene mutations and pancreatitis risk: relation to epithelial ion transport and trypsin inhibitor gene mutations.
Gastroenterology 2001;121(6):1310-9.
2001: Maimoona A Zariwala; Peadar G Noone; Aruna Sannuti; Susan L Minnix; Z Zhou; Margaret W Leigh; Milan J Hazucha; Johnny L Carson; Michael Knowles
Germline mutations in an intermediate chain dynein cause primary ciliary dyskinesia.
American journal of respiratory cell and molecular biology 2001;25(5):577-83.
2001: Kevin W Southern; Peadar G Noone; D G Bosworth; Vicky A LeGrys; Michael Knowles; Pierre M Barker
A modified technique for measurement of nasal transepithelial potential difference in infants.
The Journal of pediatrics 2001;139(3):353-8.
2001: Peadar G Noone; Michael Knowles
'CFTR-opathies': disease phenotypes associated with cystic fibrosis transmembrane regulator gene mutations.
Respiratory research 2001;2(6):328-32.
2000: Scott H Donaldson; Eduardo R Lazarowski; Maryse Picher; Michael Knowles; Monroe Stutts; Richard C Boucher
Basal nucleotide levels, release, and metabolism in normal and cystic fibrosis airways.
Molecular medicine (Cambridge, Mass.) 2000;6(11):969-82.
2000: Peadar G Noone; C A Pue; Z Zhou; Kenneth Friedman; E L Wakeling; M Ganeshananthan; Richard H Simon; Lawrence M Silverman; Michael Knowles
Lung disease associated with the IVS8 5T allele of the CFTR gene.
American journal of respiratory and critical care medicine 2000;162(5):1919-24.
2000: JA Regnis; Kirby L Zeman; Peadar G Noone; Michael Knowles; William D Bennett
Prolonged airway retention of insoluble particles in cystic fibrosis versus primary ciliary dyskinesia.
Experimental lung research 2000;26(3):149-62.
2000: Peadar G Noone; Kathy Hohneker; Z Zhou; Larry G Johnson; C Foy; C Gipson; K Jones; Terry L Noah; Margaret W Leigh; C Schwartzbach; J Efthimiou; R Pearlman; Richard C Boucher; Michael Knowles
Safety and biological efficacy of a lipid-CFTR complex for gene transfer in the nasal epithelium of adult patients with cystic fibrosis.
Molecular therapy : the journal of the American Society of Gene Therapy 2000;1(1):105-14.
1999: Kenneth Friedman; Jolanta Kole; Jonathan A Cohn; Michael Knowles; Lawrence M Silverman; Ryszard Kole
Correction of aberrant splicing of the cystic fibrosis transmembrane conductance regulator (CFTR) gene by antisense oligonucleotides.
The Journal of biological chemistry 1999;274(51):36193-9.
1999: Eitan Kerem; Tzvy Bistritzer; Aaron Hanukoglu; T Hofmann; Z Zhou; W Bennett; E MacLaughlin; P Barker; M Nash; L Quittell; Richard C Boucher; Michael Knowles
Pulmonary epithelial sodium-channel dysfunction and excess airway liquid in pseudohypoaldosteronism.
The New England journal of medicine 1999;341(3):156-62.
1999: Peadar G Noone; William D Bennett; JA Regnis; Kirby L Zeman; Johnny L Carson; M King; Richard C Boucher; Michael Knowles
Effect of aerosolized uridine-5'-triphosphate on airway clearance with cough in patients with primary ciliary dyskinesia.
American journal of respiratory and critical care medicine 1999;160(1):144-9.
1999: N M Concessio; M M VanOort; Michael Knowles; Anthony J Hickey
Pharmaceutical dry powder aerosols: correlation of powder properties with dose delivery and implications for pharmacodynamic effect.
Pharmaceutical research 1999;16(6):828-34.
1999: Peadar G Noone; D Bali; Johnny L Carson; Aruna Sannuti; C L Gipson; Lawrence E Ostrowski; Philip A Bromberg; Richard C Boucher; Michael Knowles
Discordant organ laterality in monozygotic twins with primary ciliary dyskinesia.
American journal of medical genetics 1999;82(2):155-60.
1998: Jonathan A Cohn; Kenneth Friedman; Peadar G Noone; Michael Knowles; Lawrence M Silverman; Paul S Jowell
Relation between mutations of the cystic fibrosis gene and idiopathic pancreatitis.
The New England journal of medicine 1998;339(10):653-8.
1998: George M Brinson; Peadar G Noone; Matthew A Mauro; Michael Knowles; James R Yankaskas; J S Sandhu; Paul F Jaques
Bronchial artery embolization for the treatment of hemoptysis in patients with cystic fibrosis.
American journal of respiratory and critical care medicine 1998;157(6 Pt 1):1951-8.
1998: T Hofmann; Monroe Stutts; A Ziersch; C Rückes; Wolf-Michael Weber; Michael Knowles; Hermann Lindemann; Richard C Boucher
Effects of topically delivered benzamil and amiloride on nasal potential difference in cystic fibrosis.
American journal of respiratory and critical care medicine 1998;157(6 Pt 1):1844-9.
1998: David C Wilson; Lynda Ellis; Julian Zielenski; Mary Corey; Wan F Ip; Lap-Chee Tsui; Elizabeth Tullis; Michael Knowles; Peter Roy Durie
Uncertainty in the diagnosis of cystic fibrosis: possible role of in vivo nasal potential difference measurements.
The Journal of pediatrics 1998;132(4):596-9.
1998: Ada Hamosh; Stacey C FitzSimmons; Milan Macek Jr.; Michael Knowles; Beryl J Rosenstein; Garry R Cutting
Comparison of the clinical manifestations of cystic fibrosis in black and white patients.
The Journal of pediatrics 1998;132(2):255-9.
1998: Michael Knowles; Peadar G Noone; Kathy Hohneker; Larry G Johnson; Richard C Boucher; J Efthimiou; C Crawford; R Brown; C Schwartzbach; R Pearlman
A double-blind, placebo controlled, dose ranging study to evaluate the safety and biological efficacy of the lipid-DNA complex GR213487B in the nasal epithelium of adult patients with cystic fibrosis.
Human gene therapy 1998;9(2):249-69.
1997: Mary Corey; L Edwards; H Levison; Michael Knowles
Longitudinal analysis of pulmonary function decline in patients with cystic fibrosis.
The Journal of pediatrics 1997;131(6):809-14.
1997: Michael Knowles; J M Robinson; RE Wood; C A Pue; W M Mentz; G C Wager; John Gatzy Jr; Richard C Boucher
Ion composition of airway surface liquid of patients with cystic fibrosis as compared with normal and disease-control subjects.
The Journal of clinical investigation 1997;100(10):2588-95.
1997: Peadar G Noone; JA Regnis; X Liu; Kim L R Brouwer; M Robinson; Lloyd J Edwards; Michael Knowles
Airway deposition and clearance and systemic pharmacokinetics of amiloride following aerosolization with an ultrasonic nebulizer to normal airways.
Chest 1997;112(5):1283-90.
1997: Susan Whittier; K Olivier; Peter H Gilligan; Michael Knowles; Phyllis Della-Latta
Proficiency testing of clinical microbiology laboratories using modified decontamination procedures for detection of nontuberculous mycobacteria in sputum samples from cystic fibrosis patients. The Nontuberculous Mycobacteria in Cystic Fibrosis Study Group.
Journal of clinical microbiology 1997;35(10):2706-8.
1997: Milan Macek Jr.; A Mackova; Ada Hamosh; B C Hilman; R F Selden; G Lucotte; Kenneth Friedman; Michael Knowles; Beryl J Rosenstein; Garry R Cutting
Identification of common cystic fibrosis mutations in African-Americans with cystic fibrosis increases the detection rate to 75%.
American journal of human genetics 1997;60(5):1122-7.
1997: K M Jones; E Liao; Kathy Hohneker; S Turpin; Marianna Henry; K Selinger; P H Hsyu; Richard C Boucher; Michael Knowles; G E Dukes
Pharmacokinetics of amiloride after inhalation and oral administration in adolescents and adults with cystic fibrosis.
Pharmacotherapy 1997;17(2):263-70.
1997: Pierre M Barker; C W Gowen; EDWARD LAWSON; Michael Knowles
Decreased sodium ion absorption across nasal epithelium of very premature infants with respiratory distress syndrome.
The Journal of pediatrics 1997;130(3):373-7.
1997: Kenneth Friedman; Ruth A Heim; Michael Knowles; Lawrence M Silverman
Rapid characterization of the variable length polythymidine tract in the cystic fibrosis (CFTR) gene: association of the 5T allele with selected CFTR mutations and its incidence in atypical sinopulmonary disease.
Human mutation 1997;10(2):108-15.
1997: W Edward Highsmith; L H Burch; Z Zhou; John C Olsen; T V Strong; T Smith; Kenneth Friedman; Lawrence M Silverman; Richard C Boucher; Francis S Collins; Michael Knowles
Identification of a splice site mutation (2789 +5 G > A) associated with small amounts of normal CFTR mRNA and mild cystic fibrosis.
Human mutation 1997;9(4):332-8.
1996: K N Olivier; James R Yankaskas; Michael Knowles
Nontuberculous mycobacterial pulmonary disease in cystic fibrosis.
Seminars in respiratory infections 1996;11(4):272-84.
1996: K N Olivier; William D Bennett; Kathy Hohneker; Kirby L Zeman; Lloyd J Edwards; Richard C Boucher; Michael Knowles
Acute safety and effects on mucociliary clearance of aerosolized uridine 5'-triphosphate +/- amiloride in normal human adults.
American journal of respiratory and critical care medicine 1996;154(1):217-23.
1996: William D Bennett; K N Olivier; Kirby L Zeman; Kathy Hohneker; Richard C Boucher; Michael Knowles
Effect of uridine 5'-triphosphate plus amiloride on mucociliary clearance in adult cystic fibrosis.
American journal of respiratory and critical care medicine 1996;153(6 Pt 1):1796-801.
1996: R Pinto-Powell; K N Olivier; Bryan J Marsh; Scott H Donaldson; H W Parker; W Boyle; Michael Knowles; M Magnusson; C Fordham von Reyn
Skin testing with Mycobacterium avium sensitin to identify infection with M. avium complex in patients with cystic fibrosis.
Clinical infectious diseases : an official publication of the Infectious Diseases Society of America 1996;22(3):560-2.
1996: R A Pleasants; E L Michalets; Dennis M Williams; W M Samuelson; J R Rehm; Michael Knowles
Pharmacokinetics of vancomycin in adult cystic fibrosis patients.
Antimicrobial agents and chemotherapy 1996;40(1):186-90.
1995: Kenneth Friedman; H Teichtahl; David M de Kretser; Peter D Temple-Smith; Graeme J Southwick; Lawrence M Silverman; W Edward Highsmith; Richard C Boucher; Michael Knowles
Screening Young syndrome patients for CFTR mutations.
American journal of respiratory and critical care medicine 1995;152(4 Pt 1):1353-7.
1995: Michael Knowles; Kathy Hohneker; Z Zhou; John C Olsen; Terry L Noah; P C Hu; Margaret W Leigh; J F Engelhardt; Lloyd J Edwards; K R Jones
A controlled study of adenoviral-vector-mediated gene transfer in the nasal epithelium of patients with cystic fibrosis.
The New England journal of medicine 1995;333(13):823-31.
1995: L H Burch; C R Talbot; Michael Knowles; Cecilia M Canessa; Bernard C Rossier; Richard C Boucher
Relative expression of the human epithelial Na+ channel subunits in normal and cystic fibrosis airways.
The American journal of physiology 1995;269(2 Pt 1):C511-8.
1995: Richard C Boucher; I A Gilbert; J C Hogg; M King; Michael Knowles; J Nadel
Nonmuscular airway obstruction and asthma.
American journal of respiratory and critical care medicine 1995;152(1):408-10.
1995: Michael Knowles; Anthony M Paradiso; Richard C Boucher
In vivo nasal potential difference: techniques and protocols for assessing efficacy of gene transfer in cystic fibrosis.
Human gene therapy 1995;6(4):445-55.
1995: Michael Knowles; K Olivier; Peadar G Noone; Richard C Boucher
Pharmacologic modulation of salt and water in the airway epithelium in cystic fibrosis.
American journal of respiratory and critical care medicine 1995;151(3 Pt 2):S65-9.
1995: Michael Knowles; K N Olivier; Kathy Hohneker; J Robinson; William D Bennett; Richard C Boucher
Pharmacologic treatment of abnormal ion transport in the airway epithelium in cystic fibrosis.
Chest 1995;107(2 Suppl):71S-76S.
1995: Michael Knowles
New therapies for cystic fibrosis. Introduction.
Chest 1995;107(2 Suppl):59S-60S.
1994: Richard C Boucher; Michael Knowles; Larry G Johnson; John C Olsen; Raymond J Pickles; J M Wilson; J Engelhardt; Y Yang; M Grossman
Gene therapy for cystic fibrosis using E1-deleted adenovirus: a phase I trial in the nasal cavity. The University of North Carolina at Chapel Hill.
Human gene therapy 1994;5(5):615-39.
1994: R E Wood; Michael Knowles
Recent advances in aerosol therapy.
Journal of aerosol medicine : the official journal of the International Society for Aerosols in Medicine 1994;7(1):1-11.
1994: Peadar G Noone; K N Olivier; Michael Knowles
Modulation of the ionic milieu of the airway in health and disease.
Annual review of medicine 1994;45():421-34.
1993: R P Tomkiewicz; EM App; J G Zayas; O Ramirez; N Church; Richard C Boucher; Michael Knowles; M King
Amiloride inhalation therapy in cystic fibrosis. Influence on ion content, hydration, and rheology of sputum.
The American review of respiratory disease 1993;148(4 Pt 1):1002-7.
1993: M S Cohen; Michael Knowles; James R Yankaskas
Infection due to Pseudomonas cepacia.
Clinical infectious diseases : an official publication of the Infectious Diseases Society of America 1993;17(2):291-2.
1993: Susan Whittier; R L Hopfer; Michael Knowles; Peter H Gilligan
Improved recovery of mycobacteria from respiratory secretions of patients with cystic fibrosis.
Journal of clinical microbiology 1993;31(4):861-4.
1993: Barbara R Grubb; Eduardo R Lazarowski; Michael Knowles; Richard C Boucher
Isobutylmethylxanthine fails to stimulate chloride secretion in cystic fibrosis airway epithelia.
American journal of respiratory cell and molecular biology 1993;8(4):454-60.
1993: Christian Bailly; Alan W Cuthbert; D Gentle; Michael Knowles; Michael J Waring
Sequence-selective binding of amiloride to DNA.
Biochemistry 1993;32(10):2514-24.
1993: Daniel V Schidlow; L M Taussig; Michael Knowles
Cystic Fibrosis Foundation consensus conference report on pulmonary complications of cystic fibrosis.
Pediatric pulmonology 1993;15(3):187-98.
1993: Peadar G Noone; Michael Knowles
Trends in therapy of abnormal airway epithelial ion and liquid transport.
Monaldi archives for chest disease = Archivio Monaldi per le malattie del torace / Fondazione clinica del lavoro, IRCCS [and] Istituto di clinica tisiologica e malattie apparato respiratorio, Università di Napoli, Secondo ateneo 1993;48(2):140-3.
1992: J. Michael Kilby; Peter H Gilligan; James R Yankaskas; W Edward Highsmith; Lloyd J Edwards; Michael Knowles
Nontuberculous mycobacteria in adult patients with cystic fibrosis.
Chest 1992;102(1):70-5.
1992: Michael Knowles; L L Clarke; Richard C Boucher
Extracellular ATP and UTP induce chloride secretion in nasal epithelia of cystic fibrosis patients and normal subjects in vivo.
Chest 1992;101(3 Suppl):60S-63S.
1991: Michael Knowles; L L Clarke; Richard C Boucher
Activation by extracellular nucleotides of chloride secretion in the airway epithelia of patients with cystic fibrosis.
The New England journal of medicine 1991;325(8):533-8.
1991: C W Gowen; M A Gowen; Michael Knowles
Colonic transepithelial potential difference in infants with cystic fibrosis.
The Journal of pediatrics 1991;118(3):412-5.
1991: Arthur L Beaudet; Gerald L Feldman; K Kobayashi; W K Lemna; S D Fernbach; Michael Knowles; Richard C Boucher; William E O'Brien
Mutation analysis for cystic fibrosis in a North American population.
Advances in experimental medicine and biology 1991;290():53-4.
1991: Michael Knowles; N L Church; W E Waltner; James R Yankaskas; Peter H Gilligan; M King; Lloyd J Edwards; R W Helms; Richard C Boucher
Aerosolized amiloride as treatment of cystic fibrosis lung disease: a pilot study.
Advances in experimental medicine and biology 1991;290():119-28; discussion 129-32.
1991: Richard C Boucher; T Chinet; N Willumsen; Michael Knowles; Monroe Stutts
Ion transport in normal and CF airway epithelia.
Advances in experimental medicine and biology 1991;290():105-15; discussion 115-8.
1990: W Edward Highsmith; G L Chong; H T Orr; T R Perry; D Schald; Rosann A Farber; K Wagner; Michael Knowles; W J Warwick; Lawrence M Silverman
Frequency of the delta Phe508 mutation and correlation with XV.2c/KM-19 haplotypes in an American population of cystic fibrosis patients: results of a collaborative study.
Clinical chemistry 1990;36(10):1741-6.
1990: K Kobayashi; Michael Knowles; Richard C Boucher; William E O'Brien; Arthur L Beaudet
Benign missense variations in the cystic fibrosis gene.
American journal of human genetics 1990;47(4):611-5.
1990: R A Pleasants; D M Williams; W E Waltner; Michael Knowles
Influence of infusion method on serum tobramycin concentrations in adults with cystic fibrosis.
Clinical pharmacy 1990;9(7):541-5.
1990: Johnny L Carson; Albert M Collier; Todd M Gambling; Michael Knowles; Richard C Boucher
Ultrastructure of airway epithelial cell membranes among patients with cystic fibrosis.
Human pathology 1990;21(6):640-7.
1990: Michael Knowles; N L Church; W E Waltner; James R Yankaskas; Peter H Gilligan; M King; Lloyd J Edwards; R W Helms; Richard C Boucher
A pilot study of aerosolized amiloride for the treatment of lung disease in cystic fibrosis.
The New England journal of medicine 1990;322(17):1189-94.
1989: Allyn McConkie-Rosell; Yuan-Tsong Chen; D Harris; Marcy C Speer; Margaret Pericak-Vance; Jia-huan Ding; W Edward Highsmith; Michael Knowles; SG Kahler
Mild cystic fibrosis linked to chromosome 7q22 markers with an uncommon haplotype.
Annals of internal medicine 1989;111(10):797-801.
1989: Richard C Boucher; E H Cheng; Anthony M Paradiso; Monroe Stutts; Michael Knowles; Henry Earp
Chloride secretory response of cystic fibrosis human airway epithelia. Preservation of calcium but not protein kinase C- and A-dependent mechanisms.
The Journal of clinical investigation 1989;84(5):1424-31.
1989: Michael Knowles; T B Barnett; Allyn McConkie-Rosell; C Sawyer; SG Kahler
Mild cystic fibrosis in a consanguineous family.
Annals of internal medicine 1989;110(8):599-605.
1989: Roy C Orlando; Don W Powell; R D Croom; H M Berschneider; Richard C Boucher; Michael Knowles
Colonic and esophageal transepithelial potential difference in cystic fibrosis.
Gastroenterology 1989;96(4):1041-8.
1988: Richard C Boucher; C U Cotton; John Gatzy Jr; Michael Knowles; James R Yankaskas
Evidence for reduced Cl- and increased Na+ permeability in cystic fibrosis human primary cell cultures.
The Journal of physiology 1988;405():77-103.
1988: C W Gowen; EDWARD LAWSON; J Gingras; Richard C Boucher; John Gatzy Jr; Michael Knowles
Electrical potential difference and ion transport across nasal epithelium of term neonates: correlation with mode of delivery, transient tachypnea of the newborn, and respiratory rate.
The Journal of pediatrics 1988;113(1 Pt 1):121-7.
1988: H M Berschneider; Michael Knowles; R G Azizkhan; Richard C Boucher; Nelia Tobey; Roy C Orlando; Don W Powell
Altered intestinal chloride transport in cystic fibrosis.
FASEB journal : official publication of the Federation of American Societies for Experimental Biology 1988;2(10):2625-9.
1988: Michael Knowles; G W Fernald
Diabetes and cystic fibrosis: new questions emerging from increased longevity.
The Journal of pediatrics 1988;112(3):415-6.
1987: C U Cotton; Monroe Stutts; Michael Knowles; John Gatzy Jr; Richard C Boucher
Abnormal apical cell membrane in cystic fibrosis respiratory epithelium. An in vitro electrophysiologic analysis.
The Journal of clinical investigation 1987;79(1):80-5.
1987: T B Barnett; Michael Knowles
Diffuse bacterial bronchiolitis with bronchiolar pneumonia in adults.
Southern medical journal 1987;80(1):10-5.
1987: R C Boucher; James R Yankaskas; C U Cotton; Michael Knowles; Monroe Stutts
Cell culture approaches to the investigation of human airway ion transport.
European journal of respiratory diseases. Supplement 1987;153():59-67.
1987: Richard C Boucher; C U Cotton; Monroe Stutts; Michael Knowles; John Gatzy Jr
Is cystic fibrosis respiratory epithelium characterized by a single defect (Cl-) or multiple ion transport defects?
Progress in clinical and biological research 1987;254():89-100.
1987: James R Yankaskas; Monroe Stutts; C U Cotton; Michael Knowles; John Gatzy Jr; Richard C Boucher
Cystic fibrosis airway epithelial cells in primary culture: disease-specific ion transport abnormalities.
Progress in clinical and biological research 1987;254():139-49.
1986: Monroe Stutts; Michael Knowles; John Gatzy Jr; Richard C Boucher
Oxygen consumption and ouabain binding sites in cystic fibrosis nasal epithelium.
Pediatric research 1986;20(12):1316-20.
1986: Richard C Boucher; Monroe Stutts; Michael Knowles; L Cantley; John Gatzy Jr
Na+ transport in cystic fibrosis respiratory epithelia. Abnormal basal rate and response to adenylate cyclase activation.
The Journal of clinical investigation 1986;78(5):1245-52.
1986: Monroe Stutts; J H Schwab; M G Chen; Michael Knowles; Richard C Boucher
Effects of Pseudomonas aeruginosa on bronchial epithelial ion transport.
The American review of respiratory disease 1986;134(1):17-21.
1986: Michael Knowles; Monroe Stutts; James R Yankaskas; John Gatzy Jr; Richard C Boucher
Abnormal respiratory epithelial ion transport in cystic fibrosis.
Clinics in chest medicine 1986;7(2):285-97.
1986: C W Gowen; EDWARD LAWSON; J Gingras-Leatherman; John Gatzy Jr; Richard C Boucher; Michael Knowles
Increased nasal potential difference and amiloride sensitivity in neonates with cystic fibrosis.
The Journal of pediatrics 1986;108(4):517-21.
1986: Monroe Stutts; John Gatzy Jr; Michael Knowles; C U Cotton; Richard C Boucher
Effects of formaldehyde on bronchial ion transport.
Toxicology and applied pharmacology 1986;82(2):360-7.
1985: James R Yankaskas; C U Cotton; Michael Knowles; John Gatzy Jr; Richard C Boucher
Culture of human nasal epithelial cells on collagen matrix supports. A comparison of bioelectric properties of normal and cystic fibrosis epithelia.
The American review of respiratory disease 1985;132(6):1281-7.
1985: Monroe Stutts; C U Cotton; James R Yankaskas; E Cheng; Michael Knowles; John Gatzy Jr; Richard C Boucher
Chloride uptake into cultured airway epithelial cells from cystic fibrosis patients and normal individuals.
Proceedings of the National Academy of Sciences of the United States of America 1985;82(19):6677-81.
1985: Reen Wu; James R Yankaskas; E Cheng; Michael Knowles; Richard C Boucher
Growth and differentiation of human nasal epithelial cells in culture. Serum-free, hormone-supplemented medium and proteoglycan synthesis.
The American review of respiratory disease 1985;132(2):311-20.
1985: Michael Knowles; John Gatzy Jr; Richard C Boucher
Aldosterone metabolism and transepithelial potential difference in normal and cystic fibrosis subjects.
Pediatric research 1985;19(7):676-9.
1985: James R Yankaskas; Michael Knowles; John Gatzy Jr; Richard C Boucher
Persistence of abnormal chloride ion permeability in cystic fibrosis nasal epithelial cells in heterologous culture.
Lancet 1985;1(8435):954-6.
1984: Richard C Boucher; D W Ross; Michael Knowles; John Gatzy Jr; J C Parker
Cl- permeabilities in red blood cells and peripheral blood lymphocytes from cystic fibrosis and control subjects.
Pediatric research 1984;18(12):1336-9.
1984: Michael Knowles; G Murray; J Shallal; F Askin; V Ranga; John Gatzy Jr; Richard C Boucher
Bioelectric properties and ion flow across excised human bronchi.
Journal of applied physiology: respiratory, environmental and exercise physiology 1984;56(4):868-77.
1983: Michael Knowles; Monroe Stutts; A Spock; N Fischer; John Gatzy Jr; Richard C Boucher
Abnormal ion permeation through cystic fibrosis respiratory epithelium.
Science (New York, N.Y.) 1983;221(4615):1067-70.
1983: Michael Knowles; John Gatzy Jr; Richard C Boucher
Relative ion permeability of normal and cystic fibrosis nasal epithelium.
The Journal of clinical investigation 1983;71(5):1410-7.
1982: A I Ally; R Boucher; Michael Knowles; T E Eling
Metabolism of prostaglandin endoperoxide by microsomes from human lung parenchyma and comparison with metabolites produced by pig, bovine, rat, mouse and guinea-pig.
Prostaglandins 1982;24(4):575-84.
1982: Michael Knowles; W H Buntin; Philip A Bromberg; John Gatzy Jr; Richard C Boucher
Measurements of transepithelial electric potential differences in the trachea and bronchi of human subjects in vivo.
The American review of respiratory disease 1982;126(1):108-12.
1981: Michael Knowles; John Gatzy Jr; Richard C Boucher
Increased bioelectric potential difference across respiratory epithelia in cystic fibrosis.
The New England journal of medicine 1981;305(25):1489-95.
1981: Johnny L Carson; Albert M Collier; Michael Knowles; R C Boucher; J G Rose
Morphometric aspects of ciliary distribution and ciliogenesis in human nasal epithelium.
Proceedings of the National Academy of Sciences of the United States of America 1981;78(11):6996-9.
1981: Michael Knowles; Johnny L Carson; Albert M Collier; John Gatzy Jr; Richard C Boucher
Measurements of nasal transepithelial electric potential differences in normal human subjects in vivo.
The American review of respiratory disease 1981;124(4):484-90.