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Keith Josephs

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TOP 3
Marla B Bruns; Keith A Josephs
Neuropsychiatry of corticobasal degeneration and progressive supranuclear palsy.
Jennifer L Whitwell; Joseph R Duffy; Scott D Z Eggers; Jeffrey L Gunter; Clifford R Jack; Kejal Kantarci; Mary Machulda; M L Senjem; Edythe A Strand; Keith A Josephs
Neuroimaging comparison of primary progressive apraxia of speech and progressive supranuclear palsy.
Elizabeth A Coon; Jasper R Daube; Mariely Dejesus-Hernandez; Dennis W Dickson; Robert J Ivnik; Kris A Johnson; Keith A Josephs; David S Knopman; Joseph E Parisi; Ronald C Petersen; Rosa Rademakers; Rodolfo Savica; Anahita Adeli; Matthew C Baker; Kevin B Boylan; Bradley F Boeve
Clinical and electrophysiologic variability in amyotrophic lateral sclerosis within a kindred harboring the C9ORF72 repeat expansion.

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All Publications

2013: Marla B Bruns; Keith A Josephs
Neuropsychiatry of corticobasal degeneration and progressive supranuclear palsy.
International review of psychiatry (Abingdon, England) 2013;25(2):197-209.
2013: Jennifer L Whitwell; Joseph R Duffy; Scott D Z Eggers; Jeffrey L Gunter; Clifford R Jack; Kejal Kantarci; Mary Machulda; M L Senjem; Edythe A Strand; Keith A Josephs
Neuroimaging comparison of primary progressive apraxia of speech and progressive supranuclear palsy.
European journal of neurology : the official journal of the European Federation of Neurological Societies 2013;20(4):629-37.
2013: Elizabeth A Coon; Jasper R Daube; Mariely Dejesus-Hernandez; Dennis W Dickson; Robert J Ivnik; Kris A Johnson; Keith A Josephs; David S Knopman; Joseph E Parisi; Ronald C Petersen; Rosa Rademakers; Rodolfo Savica; Anahita Adeli; Matthew C Baker; Kevin B Boylan; Bradley F Boeve
Clinical and electrophysiologic variability in amyotrophic lateral sclerosis within a kindred harboring the C9ORF72 repeat expansion.
Amyotrophic lateral sclerosis & frontotemporal degeneration 2013;14(2):132-7.
2013: Keith A Josephs; David S Knopman; Melissa E Murray; Joseph E Parisi; Ronald C Petersen; Rosa Rademakers; Matthew L Senjem; Jennifer L Whitwell; Bradley F Boeve; Neill R Graff-Radford; Clifford R Jack; Dennis W Dickson
Corticospinal tract degeneration associated with TDP-43 type C pathology and semantic dementia.
Brain : a journal of neurology 2013;136(Pt 2):455-70.
2013: Jennifer L Whitwell; Jia Xu; Bradley F Boeve; Dennis W Dickson; Clifford R Jack; David S Knopman; Jay Mandrekar; Joseph E Parisi; Ronald C Petersen; Rosa Rademakers; Matthew L Senjem; Keith A Josephs
Frontal asymmetry in behavioral variant frontotemporal dementia: clinicoimaging and pathogenetic correlates.
Neurobiology of aging 2013;34(2):636-9.
2013: Ajay Madhavan; Ronald C Petersen; Matthew L Senjem; Edythe A Strand; Nirubol Tosakulwong; Stephen D Weigand; Jennifer L Whitwell; Joseph R Duffy; Jeffrey L Gunter; Clifford R Jack; Val J Lowe; Mary Machulda; Keith A Josephs
FDG PET and MRI in Logopenic Primary Progressive Aphasia versus Dementia of the Alzheimer's Type.
PloS one 2013;8(4):e62471.
2013: Florence C F Chang; Keith A Josephs
Levodopa Responsiveness in Adult-onset Lower Limb Dystonia is Associated with the Development of Parkinson's Disease.
Tremor and other hyperkinetic movements (New York, N.Y.) 2013;3():.
2012: Jennifer L Whitwell; Keith A Josephs
Recent advances in the imaging of frontotemporal dementia.
Current neurology and neuroscience reports 2012;12(6):715-23.
2012: Jonathan Graff-Radford; David S Knopman; Ronald C Petersen; J Eric Ahlskog; Bradley F Boeve; Daniel A Drubach; Dina I Drubach; Erin C Golden; Keith A Josephs
Limb immobilization and corticobasal syndrome.
Parkinsonism & related disorders 2012;18(10):1097-9.
2012: Jennifer L Whitwell; Jia Xu; Jeffrey L Gunter; Clifford R Jack; Jay Mandrekar; Keith A Josephs
Imaging measures predict progression in progressive supranuclear palsy.
Movement disorders : official journal of the Movement Disorder Society 2012;27(14):1801-4.
2012: Keith A Josephs; Scott D Z Eggers; Clifford R Jack; Jennifer L Whitwell
Neuroanatomical correlates of the progressive supranuclear palsy corticobasal syndrome hybrid.
European journal of neurology : the official journal of the European Federation of Neurological Societies 2012;19(11):1440-6.
2012: Jennifer L Whitwell; Bradley F Boeve; Dennis W Dickson; Clifford R Jack; David S Knopman; Melissa E Murray; Joseph E Parisi; Ronald C Petersen; Matthew L Senjem; Nirubol Tosakulwong; Stephen D Weigand; Keith A Josephs
Neuroimaging correlates of pathologically defined subtypes of Alzheimer's disease: a case-control study.
Lancet neurology 2012;11(10):868-77.
2012: Jonathan Graff-Radford; Joseph R Duffy; Edythe A Strand; Keith A Josephs
Parkinsonian motor features distinguish the agrammatic from logopenic variant of primary progressive aphasia.
Parkinsonism & related disorders 2012;18(7):890-2.
2012: Elizabeth A Coon; Clifford R Jack; Jennifer L Whitwell; Keith A Josephs
Primary lateral sclerosis as progressive supranuclear palsy: diagnosis by diffusion tensor imaging.
Movement disorders : official journal of the Movement Disorder Society 2012;27(7):903-6.
2012: D C Perry; Ronald C. Petersen; Jennifer L Whitwell; Bradley Boeve; Clifford R Jack; David S. Knopman; V Shane Pankratz; Keith A Josephs
Voxel-based morphometry in patients with obsessive-compulsive behaviors in behavioral variant frontotemporal dementia.
European journal of neurology : the official journal of the European Federation of Neurological Societies 2012;19(6):911-7.
2012: E P Flanagan; C M Harper; M H Silber; E K St Louis; Keith A Josephs
Amiodarone-associated neuromyopathy: a report of four cases.
European journal of neurology : the official journal of the European Federation of Neurological Societies 2012;19(5):e50-1.
2012: Keith A Josephs; Val J Lowe; Mary Machulda; Ankit V Master; Matthew L Senjem; Edythe A Strand; Joseph R Duffy; Clifford R Jack; Jennifer L Whitwell
Characterizing a neurodegenerative syndrome: primary progressive apraxia of speech.
Brain : a journal of neurology 2012;135(Pt 5):1522-36.
2012: Rodolfo Savica; Lester E Wold; Keith A Josephs; Joseph E Parisi; J Eric Ahlskog
High school football and risk of neurodegeneration: a community-based study.
Mayo Clinic proceedings. Mayo Clinic 2012;87(4):335-40.
2012: Jennifer L Whitwell; Jia Xu; Jeffrey L Gunter; Clifford R Jack; Jay N Mandrekar; Keith A Josephs
Rates of brain atrophy and clinical decline over 6 and 12-month intervals in PSP: determining sample size for treatment trials.
Parkinsonism & related disorders 2012;18(3):252-6.
2012: Anhar Hassan; Joseph E Parisi; Keith A Josephs
Autopsy-proven progressive supranuclear palsy presenting as behavioral variant frontotemporal dementia.
Neurocase 2012;18(6):478-88.
2011: Jonathan Graff-Radford; Clifford R Jack; Michael D Jensen; Max R Trenerry; Jennifer L Whitwell; J Eric Ahlskog; Keith A Josephs
Focal brain atrophy in gastric bypass patients with cognitive complaints.
Journal of clinical neuroscience : official journal of the Neurosurgical Society of Australasia 2011;18(12):1671-6.
2011: Melissa E Murray; Rosa Rademakers; Nicola J Rutherford; Zbigniew K Wszolek; Matt Baker; Kevin B Boylan; Mariely DeJesus-Hernandez; Ranjan Duara; Tanis J Ferman; Neill R Graff-Radford; Keith A Josephs; Dennis W Dickson
Clinical and neuropathologic heterogeneity of c9FTD/ALS associated with hexanucleotide repeat expansion in C9ORF72.
Acta neuropathologica 2011;122(6):673-90.
2011: Anhar Hassan; Jennifer L Whitwell; Keith A Josephs
The corticobasal syndrome-Alzheimer's disease conundrum.
Expert review of neurotherapeutics 2011;11(11):1569-78.
2011: Naomi Kouri; Irene Litvan; Melissa E Murray; Rosa Rademakers; Ryan Uitti; Zbigniew K Wszolek; Bradley F Boeve; Neill R Graff-Radford; Anhar Hassan; Keith A Josephs; Dennis W Dickson
Neuropathological features of corticobasal degeneration presenting as corticobasal syndrome or Richardson syndrome.
Brain : a journal of neurology 2011;134(Pt 11):3264-75.
2011: Dennis W Dickson; Naomi Kouri; Melissa E Murray; Keith A Josephs
Neuropathology of frontotemporal lobar degeneration-tau (FTLD-tau).
Journal of molecular neuroscience : MN 2011;45(3):384-9.
2011: Jennifer L Whitwell; David S Knopman; Joseph E Parisi; Ronald C Petersen; Bradley F Boeve; Dennis W Dickson; Clifford R Jack; Keith A Josephs
Imaging signatures of molecular pathology in behavioral variant frontotemporal dementia.
Journal of molecular neuroscience : MN 2011;45(3):372-8.
2011: Mariely DeJesus-Hernandez; Dennis W Dickson; Howard Feldman; NiCole A Finch; Heather Flynn; Daniel Geschwind; Neill R Graff-Radford; Ging-Yuek R Hsiung; Keith A Josephs; Anna Karydas; David S Knopman; Naomi Kouri; Ian R A Mackenzie; Bruce L Miller; Alexandra M Nicholson; Ronald C Petersen; Jennifer Adamson; Matt Baker; Bradley F Boeve; Adam L Boxer; Kevin B Boylan; Giovanni Coppola; Nicola J Rutherford; William W Seeley; Pheth Sengdy; Aleksandra Wojtas; Zbigniew K Wszolek; Rosa Rademakers
Expanded GGGGCC hexanucleotide repeat in noncoding region of C9ORF72 causes chromosome 9p-linked FTD and ALS.
Neuron 2011;72(2):245-56.
2011: Farrah Mateen; Max R Trenerry; A L Weaver; M Carone; M D Felmlee-Devine; Keith A Josephs; R D White
Long-term cognitive outcomes following out-of-hospital cardiac arrest: a population-based study.
Neurology 2011;77(15):1438-45.
2011: Katya Rascovsky; Jonathan D Rohrer; Howard Rosen; Martin N Rossor; David P Salmon; Harro Seelaar; William W Seeley; John C van Swieten; Jason D Warren; Sandra Weintraub; John Neuhaus; CHIADIKAOBI ONYIKE; Florence Pasquier; Olivier Piguet; Yolande Pijnenburg; Caroline E Prioleau-Latham; Katherine P Rankin; Sandra E Black; Bradley F Boeve; Stefano F Cappa; Tiffany W Chow; Vincent Deramecourt; Bradford C Dickerson; Janine Diehl-Schmid; Elise G P Dopper; Nick C Fox; Morris Freedman; Douglas Galasko; Maria-Luisa Gorno-Tempini; Jordan Grafman; Murray Grossman; ARGYE HILLIS-TRUPE; John R Hodges; Julene K Johnson; Keith A Josephs; Andrew Kertesz; Christopher M Kipps; David S. Knopman; Joel H Kramer; Florence Lebert; Albert Lee; Patricia Lillo; Facundo Manes; Mario F Mendez; Marsel Mesulam; Bruce L Miller
Sensitivity of revised diagnostic criteria for the behavioural variant of frontotemporal dementia.
Brain : a journal of neurology 2011;134(Pt 9):2456-77.
2011: Jennifer L Whitwell; Ankit Master; Matthew L Senjem; Prashanthi Vemuri; Rajeswari Avula; Clifford R Jack; David T Jones; Keith A Josephs
Disrupted thalamocortical connectivity in PSP: a resting-state fMRI, DTI, and VBM study.
Parkinsonism & related disorders 2011;17(8):599-605.
2011: Rodolfo Savica; Alejandro A Rabinstein; Keith A Josephs
Ifosfamide associated myoclonus-encephalopathy syndrome.
Journal of neurology 2011;258(9):1729-31.
2011: Jennifer L Whitwell; Bradley F Boeve; dennis dickson; Clifford R Jack; David S. Knopman; Joseph E Parisi; Ronald C. Petersen; Scott A Przybelski; Matthew L Senjem; Keith A Josephs
Temporoparietal atrophy: a marker of AD pathology independent of clinical diagnosis.
Neurobiology of aging 2011;32(9):1531-41.
2011: Jennifer L Whitwell; Z K Wszolek; Rajeswari Avula; M Baker; Bradley Boeve; Jeffrey L Gunter; D T Jones; Keith A Josephs; David S. Knopman; Ronald C. Petersen; Rosa Rademakers; M L Senjem; N Tosakulwong; Prashanthi Vemuri; Stephen D Weigand; Clifford R Jack
Altered functional connectivity in asymptomatic MAPT subjects: a comparison to bvFTD.
Neurology 2011;77(9):866-74.
2011: Rodolfo Savica; Matt Stead; J Eric Ahlskog; Keith A Josephs; Kendall H Lee; Joseph Y Matsumoto; Bryan T Klassen
Deep brain stimulation in benign tremulous parkinsonism.
Archives of neurology 2011;68(8):1033-6.
2011: Keith A Josephs; Ian R Mackenzie; David M Mann; Manuela Neumann; Julie S Snowden; John R Hodges; dennis dickson
Neuropathological background of phenotypical variability in frontotemporal dementia.
Acta neuropathologica 2011;122(2):137-53.
2011: Jennifer L Whitwell; Z K Wszolek; M Baker; Bradley Boeve; Jeffrey L Gunter; Clifford R Jack; David S. Knopman; Ronald C. Petersen; R Rademakers; Stephen D Weigand; Keith A Josephs
Trajectories of brain and hippocampal atrophy in FTD with mutations in MAPT or GRN.
Neurology 2011;77(4):393-8.
2011: Akiyuki Tomiyasu; Shuichi Ueno; Hiroshi Ujike; Koichi Wakabayashi; Hidetaka Yamada; Tatsuo Yamada; Fusako Yokochi; Andrzej Szczudlik; Takanobu Takei; Haruhiko Tanaka; Rie Tohge; Kana Tojo; Jan Aasly; Zaid Afawi; Dusica Babovic-Vuksanovic; Ilan Blatt; Nicolas Dupré; Masaki Fujiwara; Mio Ichiba; Toshio Inui; Keith A Josephs; Hans H Jung; Yasufumi Kageyama; Yuji Kanemori; Jan Kobal; Katya Kotschet; Mizuki Morimoto; Masayuki Nakamura; Satoshi Orimo; Silvana Penco; Guilherme Riccioppo Rodrigues; Monika Rudzińska; Shinji Saiki; Akira Sano
Novel pathogenic mutations and copy number variations in the VPS13A gene in patients with chorea-acanthocytosis.
American journal of medical genetics. Part B, Neuropsychiatric genetics : the official publication of the International Society of Psychiatric Genetics 2011;156B(5):620-31.
2011: Jennifer L Whitwell; Kejal Kantarci; Ankit V Master; Ramesh Avula; Heidi A Edmonson; Scott D Eggers; Clifford R Jack; Keith A Josephs
Clinical correlates of white matter tract degeneration in progressive supranuclear palsy.
Archives of neurology 2011;68(6):753-60.
2011: Jason R Cornelius; Keith A Josephs; Vanda A Lennon; Andrew McKeon; Sean J Pittock; Paula A Aston; Maja Tippmann-Peikert; Michael H Silber
Sleep manifestations of voltage-gated potassium channel complex autoimmunity.
Archives of neurology 2011;68(6):733-8.
2011: E A Coon; E J Sorenson; J L Whitwell; David S. Knopman; Keith A Josephs
Predicting survival in frontotemporal dementia with motor neuron disease.
Neurology 2011;76(22):1886-93.
2011: Xiaofan Li; Maria I Lapid; M Caroline Burton; Keith A Josephs
Psychoses as the presenting manifestation of Creutzfeldt-Jakob disease in an elderly male.
General hospital psychiatry 2011;33(3):302.e7-9.
2011: Naomi Kouri; Jennifer L Whitwell; Keith A Josephs; Rosa Rademakers; dennis dickson
Corticobasal degeneration: a pathologically distinct 4R tauopathy.
Nature reviews. Neurology 2011;7(5):263-72.
2011: A Hassan; James H Bower; N Kumar; Joseph Y Matsumoto; R D Fealey; Keith A Josephs; J Eric Ahlskog
Dopamine agonist-triggered pathological behaviors: surveillance in the PD clinic reveals high frequencies.
Parkinsonism & related disorders 2011;17(4):260-4.
2011: Roberta Frigerio; Hiroshige Fujishiro; Tae-Beom Ahn; Keith A Josephs; Demetrius M Maraganore; Anthony DelleDonne; Joseph E Parisi; Kevin J Klos; Bradley Boeve; dennis dickson; J Eric Ahlskog
Incidental Lewy body disease: do some cases represent a preclinical stage of dementia with Lewy bodies?
Neurobiology of aging 2011;32(5):857-63.
2011: M R Wicklund; Bahram Mokri; D A Drubach; Bradley Boeve; Joseph E Parisi; Keith A Josephs
Frontotemporal brain sagging syndrome: an SIH-like presentation mimicking FTD.
Neurology 2011;76(16):1377-82.
2011: Keith A Josephs
Neuronal intranuclear inclusion disease: no longer a pain in the butt.
Neurology 2011;76(16):1368-9.
2011: Prashanthi Vemuri; Gyorgy Simon; Kejal Kantarci; Jennifer L Whitwell; Matthew L Senjem; Scott A Przybelski; Jeffrey L Gunter; Keith A Josephs; David S. Knopman; Bradley Boeve; Tanis J Ferman; dennis dickson; Joseph E Parisi; Ronald C. Petersen; Clifford R Jack
Antemortem differential diagnosis of dementia pathology using structural MRI: Differential-STAND.
NeuroImage 2011;55(2):522-31.
2011: Victoria Passov; Ralitza H Gavrilova; Edythe Strand; Jane H Cerhan; Keith A Josephs
Sporadic corticobasal syndrome with progranulin mutation presenting as progressive apraxic agraphia.
Archives of neurology 2011;68(3):376-80.
2011: Daniel O Claassen; Val J Lowe; Patrick J Peller; Ronald C. Petersen; Keith A Josephs
Amyloid and glucose imaging in dementia with Lewy bodies and multiple systems atrophy.
Parkinsonism & related disorders 2011;17(3):160-5.
2011: Keith A Josephs; Jennifer L Whitwell; Scott D Z Eggers; Matthew L Senjem; Clifford R Jack
Gray matter correlates of behavioral severity in progressive supranuclear palsy.
Movement disorders : official journal of the Movement Disorder Society 2011;26(3):493-8.
2011: Keith A Josephs; Jennifer L Whitwell; Stephen D Weigand; Matthew L Senjem; Bradley Boeve; David S. Knopman; Glenn Smith; Robert J Ivnik; Clifford R Jack; Ronald C. Petersen
Predicting functional decline in behavioural variant frontotemporal dementia.
Brain : a journal of neurology 2011;134(Pt 2):432-48.
2011: Jennifer L Whitwell; Keith A Josephs
Neuroimaging in frontotemporal lobar degeneration--predicting molecular pathology.
Nature reviews. Neurology 2011;8(3):131-42.
2011: Jannet Kocerha; Naomi Kouri; Matt Baker; Bradley F Boeve; Kumaravel Chidamparam; Julia Crook; Mariely DeJesus-Hernandez; Dennis W Dickson; NiCole Finch; John Gonzalez; Neill R Graff-Radford; Keith A Josephs; Rosa Rademakers
Altered microRNA expression in frontotemporal lobar degeneration with TDP-43 pathology caused by progranulin mutations.
BMC genomics 2011;12():527.
2010: Jennifer L Whitwell; Clifford R Jack; Joseph E Parisi; M L Senjem; David S. Knopman; Bradley Boeve; Rosa Rademakers; M Baker; Ronald C. Petersen; dennis dickson; Keith A Josephs
Does TDP-43 type confer a distinct pattern of atrophy in frontotemporal lobar degeneration?
Neurology 2010;75(24):2212-20.
2010: Jonathan Graff-Radford; J Eric Ahlskog; James H Bower; Keith A Josephs
Dopamine agonists and Othello's syndrome.
Parkinsonism & related disorders 2010;16(10):680-2.
2010: J L Whitwell; C R Jack; B F Boeve; Joseph E Parisi; J E Ahlskog; D A Drubach; M L Senjem; David S. Knopman; Ronald C. Petersen; dennis dickson; Keith A Josephs
Imaging correlates of pathology in corticobasal syndrome.
Neurology 2010;75(21):1879-87.
2010: Eoin P Flanagan; Andrew McKeon; Vanda A Lennon; Bradley F Boeve; Max R Trenerry; K Meng Tan; Daniel A Drubach; Keith A Josephs; Jeffrey W Britton; Jayawant N Mandrekar; Val Lowe; Joseph E Parisi; Sean J Pittock
Autoimmune dementia: clinical course and predictors of immunotherapy response.
Mayo Clinic proceedings. Mayo Clinic 2010;85(10):881-97.
2010: Keith A Josephs
Dementia and the TAR DNA binding protein 43.
Clinical pharmacology and therapeutics 2010;88(4):555-8.
2010: Keith A Josephs; Jennifer L Whitwell
Parkinson disease and down in the dumps: pumped or stumped?
Neurology 2010;75(10):846-7.
2010: D O Claassen; Keith A Josephs; J Eric Ahlskog; M H Silber; M Tippmann-Peikert; B F Boeve
REM sleep behavior disorder preceding other aspects of synucleinopathies by up to half a century.
Neurology 2010;75(6):494-9.
2010: dennis dickson; Zeshan Ahmed; Avi A Algom; Yoshio Tsuboi; Keith A Josephs
Neuropathology of variants of progressive supranuclear palsy.
Current opinion in neurology 2010;23(4):394-400.
2010: Keith A Josephs; Jennifer L Whitwell; Bradley Boeve; David S. Knopman; Ronald C. Petersen; William T Hu; Joseph E Parisi; dennis dickson; Clifford R Jack
Anatomical differences between CBS-corticobasal degeneration and CBS-Alzheimer's disease.
Movement disorders : official journal of the Movement Disorder Society 2010;25(9):1246-52.
2010: Hazel Urwin; Keith A Josephs; Jonathan D Rohrer; Ian R Mackenzie; Manuela Neumann; Astrid Authier; Harro Seelaar; John C Van Swieten; Jeremy M Brown; Peter Johannsen; Jorgen E Nielsen; Ida E Holm; dennis dickson; Rosa Rademakers; Neill R Graff-Radford; Joseph E Parisi; Ronald C. Petersen; Kimmo J Hatanpaa; Charles L White; Myron F Weiner; Felix Geser; Vivianna M Van Deerlin; John Q Trojanowski; Bruce L Miller; William W Seeley; Julie van der Zee; Samir Kumar-Singh; Sebastiaan Engelborghs; Peter P De Deyn; Christine Van Broeckhoven; Eileen H Bigio; Han-Xiang Deng; Glenda M Halliday; Jillian J Kril; David G Munoz; D M A Mann; Stuart M Pickering-Brown; Valerie Doodeman; Gary Adamson; Shabnam Ghazi-Noori; Elizabeth M C Fisher; Janice L Holton; Tamas Revesz; Martin N Rossor; John Collinge; Simon Mead; Adrian M Isaacs
FUS pathology defines the majority of tau- and TDP-43-negative frontotemporal lobar degeneration.
Acta neuropathologica 2010;120(1):33-41.
2010: Keith A Josephs; Jennifer L Whitwell; Joseph E Parisi; Ronald C. Petersen; Bradley Boeve; Clifford R Jack; dennis dickson
Caudate atrophy on MRI is a characteristic feature of FTLD-FUS.
European journal of neurology : the official journal of the European Federation of Neurological Societies 2010;17(7):969-75.
2010: Keith A Josephs; Joseph R Duffy; Tepanta R Fossett; Edythe A Strand; Daniel O Claassen; Jennifer L Whitwell; Patrick J Peller
Fluorodeoxyglucose F18 positron emission tomography in progressive apraxia of speech and primary progressive aphasia variants.
Archives of neurology 2010;67(5):596-605.
2010: Jennifer L Whitwell; Rajeswari Avula; M L Senjem; Kejal Kantarci; Stephen D Weigand; A Samikoglu; H A Edmonson; Prashanthi Vemuri; David S. Knopman; Bradley Boeve; Ronald C. Petersen; Keith A Josephs; Clifford R Jack
Gray and white matter water diffusion in the syndromic variants of frontotemporal dementia.
Neurology 2010;74(16):1279-87.
2010: T F Gendron; Keith A Josephs; Leonard Petrucelli
Review: transactive response DNA-binding protein 43 (TDP-43): mechanisms of neurodegeneration.
Neuropathology and applied neurobiology 2010;36(2):97-112.
2010: Anhar Hassan; Jennifer L Whitwell; Bradley F Boeve; Clifford R Jack; Joseph E Parisi; dennis dickson; Keith A Josephs
Symmetric corticobasal degeneration (S-CBD).
Parkinsonism & related disorders 2010;16(3):208-14.
2010: Daniel O Claassen; Keith A Josephs; Patrick J Peller
The stripe of primary lateral sclerosis: focal primary motor cortex hypometabolism seen on fluorodeoxyglucose F18 positron emission tomography.
Archives of neurology 2010;67(1):122-5.
2009: dennis dickson; Hiroshige Fujishiro; Carolyn Orr; Anthony DelleDonne; Keith A Josephs; Roberta Frigerio; Melinda Burnett; Joseph E Parisi; Kevin J Klos; J Eric Ahlskog
Neuropathology of non-motor features of Parkinson disease.
Parkinsonism & related disorders 2009;15 Suppl 3():S1-5.
2009: Keith A Josephs; Jennifer L Whitwell; David S. Knopman; Bradley Boeve; Prashanthi Vemuri; M L Senjem; Joseph E Parisi; Robert J Ivnik; dennis dickson; Ronald C. Petersen; Clifford R Jack
Two distinct subtypes of right temporal variant frontotemporal dementia.
Neurology 2009;73(18):1443-50.
2009: William T Hu; Harro Seelaar; Keith A Josephs; David S. Knopman; Bradley Boeve; Eric J Sorenson; Leo McCluskey; Lauren Elman; Helenius J Schelhaas; Joseph E Parisi; Benno Kuesters; Virginia M-Y Lee; John Q Trojanowski; Ronald C. Petersen; John C van Swieten; Murray Grossman
Survival profiles of patients with frontotemporal dementia and motor neuron disease.
Archives of neurology 2009;66(11):1359-64.
2009: Jennifer L Whitwell; Scott A Przybelski; Stephen D Weigand; Robert J Ivnik; Prashanthi Vemuri; Jeffrey L Gunter; Matthew L Senjem; Maria M Shiung; Bradley Boeve; David S. Knopman; Joseph E Parisi; dennis dickson; Ronald C. Petersen; Clifford R Jack; Keith A Josephs
Distinct anatomical subtypes of the behavioural variant of frontotemporal dementia: a cluster analysis study.
Brain : a journal of neurology 2009;132(Pt 11):2932-46.
2009: Stephanie A Cobb; Christian Wider; Owen A Ross; Ignacio Mata; Charles H Adler; Alex Rajput; Ali H Rajput; Ruey-Meei Wu; Robert Hauser; Keith A Josephs; Jonathan Carr; Katrina Gwinn-Hardy; Michael G Heckman; Jan Aasly; Timothy Lynch; Ryan Uitti; Zbigniew K Wszolek; Gregory Kapatos; Matthew J Farrer
GCH1 in early-onset Parkinson's disease.
Movement disorders : official journal of the Movement Disorder Society 2009;24(14):2070-5.
2009: Jennifer L Whitwell; Clifford R Jack; Bradley Boeve; M L Senjem; M Baker; Robert J Ivnik; David S. Knopman; Zbigniew K Wszolek; Ronald C. Petersen; Rosa Rademakers; Keith A Josephs
Atrophy patterns in IVS10+16, IVS10+3, N279K, S305N, P301L, and V337M MAPT mutations.
Neurology 2009;73(13):1058-65.
2009: Roberta Frigerio; Hiroshige Fujishiro; Demetrius M Maraganore; Kevin J Klos; Anthony DelleDonne; Michael G Heckman; Julia E Crook; Keith A Josephs; Joseph E Parisi; Bradley Boeve; dennis dickson; J Eric Ahlskog
Comparison of risk factor profiles in incidental Lewy body disease and Parkinson disease.
Archives of neurology 2009;66(9):1114-9.
2009: Keith A Josephs; Alex Stroh; Brittany Dugger; dennis dickson
Evaluation of subcortical pathology and clinical correlations in FTLD-U subtypes.
Acta neuropathologica 2009;118(3):349-58.
2009: William T Hu; Gregory W Rippon; Bradley Boeve; David S. Knopman; Ronald C. Petersen; Joseph E Parisi; Keith A Josephs
Alzheimer's disease and corticobasal degeneration presenting as corticobasal syndrome.
Movement disorders : official journal of the Movement Disorder Society 2009;24(9):1375-9.
2009: Farrah Mateen; Keith A Josephs
The clinical spectrum of stereotypies in frontotemporal lobar degeneration.
Movement disorders : official journal of the Movement Disorder Society 2009;24(8):1237-40.
2009: Carles vilarino-guell; C Wider; A I Soto-Ortolaza; Stephanie A Cobb; Jennifer Kachergus; B H Keeling; J C Dachsel; Mary Hulihan; dennis dickson; Zbigniew K Wszolek; Ryan Uitti; Neill R Graff-Radford; Bradley Boeve; Keith A Josephs; Bruce L Miller; K B Boylan; Katrina Gwinn-Hardy; Charles H Adler; Jan Aasly; Faycal Hentati; Alain Destée; Anna Krygowska-Wajs; Marie-Christine Chartier-Harlin; Owen A Ross; Rosa Rademakers; Matthew J Farrer
Characterization of DCTN1 genetic variability in neurodegeneration.
Neurology 2009;72(23):2024-8.
2009: Daniel O Claassen; Keith A Josephs
Pramipexole induced compulsive behaviors abate after initiation of rotigitine.
Movement disorders : official journal of the Movement Disorder Society 2009;24(7):1090-1.
2009: Brendan J Kelley; Wael Haidar; Bradley Boeve; Matt Baker; Neill R Graff-Radford; Thomas Krefft; Andrew R Frank; Clifford R Jack; Maria M Shiung; David S. Knopman; Keith A Josephs; Sotirios A Parashos; Rosa Rademakers; Michael Hutton; Stuart Pickering-Brown; Jennifer Adamson; Karen M Kuntz; dennis dickson; Joseph E Parisi; Glenn Smith; Robert J Ivnik; Ronald C. Petersen
Prominent phenotypic variability associated with mutations in Progranulin.
Neurobiology of aging 2009;30(5):739-51.
2009: Jennifer L Whitwell; Clifford R Jack; Bradley Boeve; M L Senjem; M Baker; R Rademakers; Robert J Ivnik; David S. Knopman; Zbigniew K Wszolek; Ronald C. Petersen; Keith A Josephs
Voxel-based morphometry patterns of atrophy in FTLD with mutations in MAPT or PGRN.
Neurology 2009;72(9):813-20.
2009: Brendan J Kelley; Bradley Boeve; Keith A Josephs
Rapidly progressive young-onset dementia.
Cognitive and behavioral neurology : official journal of the Society for Behavioral and Cognitive Neurology 2009;22(1):22-7.
2009: Farrah Mateen; Keith A Josephs
TDP-43 is not present in brain tissue of patients with schizophrenia.
Schizophrenia research 2009;108(1-3):297-8.
2009: Keith A Josephs; J Eric Ahlskog; Joseph E Parisi; Bradley Boeve; Brian A Crum; Caterina Giannini; Ronald C. Petersen
Rapidly progressive neurodegenerative dementias.
Archives of neurology 2009;66(2):201-7.
2009: McKeon Andrew; J Eric Ahlskog; James H Bower; Keith A Josephs; Joseph Y Matsumoto
Psychogenic tremor: long-term prognosis in patients with electrophysiologically confirmed disease.
Movement disorders : official journal of the Movement Disorder Society 2009;24(1):72-6.
2009: Brendan J Kelley; Bradley Boeve; Keith A Josephs
Cognitive and noncognitive neurological features of young-onset dementia.
Dementia and geriatric cognitive disorders 2009;27(6):564-71.
2009: Jennifer L Whitwell; Clifford R Jack; Matthew L Senjem; Joseph E Parisi; Bradley Boeve; David S. Knopman; dennis dickson; Ronald C. Petersen; Keith A Josephs
MRI correlates of protein deposition and disease severity in postmortem frontotemporal lobar degeneration.
Neuro-degenerative diseases 2009;6(3):106-17.
2009: Alex D Cooper; Keith A Josephs
Photophobia, visual hallucinations, and REM sleep behavior disorder in progressive supranuclear palsy and corticobasal degeneration: a prospective study.
Parkinsonism & related disorders 2009;15(1):59-61.
2008: Kathrin Czarnecki; Joseph R Duffy; Carissa R Nehl; Shelley A Cross; Jennifer R Molano; Clifford R Jack; Maria M Shiung; Keith A Josephs; Bradley Boeve
Very early semantic dementia with progressive temporal lobe atrophy: an 8-year longitudinal study.
Archives of neurology 2008;65(12):1659-63.
2008: Keith A Josephs; Joseph R Duffy
Apraxia of speech and nonfluent aphasia: a new clinical marker for corticobasal degeneration and progressive supranuclear palsy.
Current opinion in neurology 2008;21(6):688-92.
2008: Rosa Rademakers; Jason Eriksen; Matt Baker; Todd Robinson; Zeshan Ahmed; Sarah J Lincoln; Nicole Finch; Nicola J Rutherford; Richard J Crook; Keith A Josephs; Bradley Boeve; David S. Knopman; Ronald C. Petersen; Joseph E Parisi; Richard Caselli; Zbigniew K Wszolek; Ryan Uitti; Howard Feldman; Michael Hutton; Ian R Mackenzie; Neill R Graff-Radford; dennis dickson
Common variation in the miR-659 binding-site of GRN is a major risk factor for TDP43-positive frontotemporal dementia.
Human molecular genetics 2008;17(23):3631-42.
2008: Keith A Josephs; Jennifer L Whitwell; Clifford R Jack
Anatomic correlates of stereotypies in frontotemporal lobar degeneration.
Neurobiology of aging 2008;29(12):1859-63.
2008: Keith A Josephs; Jennifer L Whitwell; P Vemuri; M L Senjem; Bradley Boeve; David S. Knopman; Glenn Smith; Robert J Ivnik; Ronald C. Petersen; Clifford R Jack
The anatomic correlate of prosopagnosia in semantic dementia.
Neurology 2008;71(20):1628-33.
2008: Brendan J Kelley; Bradley Boeve; Keith A Josephs
Young-onset dementia: demographic and etiologic characteristics of 235 patients.
Archives of neurology 2008;65(11):1502-8.
2008: Farrah Mateen; Keith A Josephs
Sudden behavioral disturbance in a man with a lesion in the nucleus accumbens.
Journal of neurology 2008;255(11):1834-5.
2008: Jennifer L Whitwell; Keith A Josephs; M E Murray; Kejal Kantarci; S A Przybelski; Stephen D Weigand; Prashanthi Vemuri; M L Senjem; Joseph E Parisi; David S. Knopman; Bradley Boeve; Ronald C. Petersen; dennis dickson; Clifford R Jack
MRI correlates of neurofibrillary tangle pathology at autopsy: a voxel-based morphometry study.
Neurology 2008;71(10):743-9.
2008: Daniel O Claassen; Joseph E Parisi; Caterina Giannini; Bradley Boeve; dennis dickson; Keith A Josephs
Frontotemporal dementia mimicking dementia with Lewy bodies.
Cognitive and behavioral neurology : official journal of the Society for Behavioral and Cognitive Neurology 2008;21(3):157-63.
2008: Hiroshige Fujishiro; Tae-Beom Ahn; Roberta Frigerio; Anthony DelleDonne; Keith A Josephs; Joseph E Parisi; J Eric Ahlskog; dennis dickson
Glial cytoplasmic inclusions in neurologically normal elderly: prodromal multiple system atrophy?
Acta neuropathologica 2008;116(3):269-75.
2008: Prashanthi Vemuri; Jennifer L Whitwell; Kejal Kantarci; Keith A Josephs; Joseph E Parisi; Maria S Shiung; David S. Knopman; Bradley Boeve; Ronald C. Petersen; dennis dickson; Clifford R Jack
Antemortem MRI based STructural Abnormality iNDex (STAND)-scores correlate with postmortem Braak neurofibrillary tangle stage.
NeuroImage 2008;42(2):559-67.
2008: Anthony DelleDonne; Kevin J Klos; Hiroshige Fujishiro; Zeshan Ahmed; Joseph E Parisi; Keith A Josephs; Roberta Frigerio; Melinda Burnett; Zbigniew K Wszolek; Ryan Uitti; J Eric Ahlskog; dennis dickson
Incidental Lewy body disease and preclinical Parkinson disease.
Archives of neurology 2008;65(8):1074-80.
2008: William T Hu; Keith A Josephs; David S. Knopman; Bradley Boeve; dennis dickson; Ronald C. Petersen; Joseph E Parisi
Temporal lobar predominance of TDP-43 neuronal cytoplasmic inclusions in Alzheimer disease.
Acta neuropathologica 2008;116(2):215-20.
2008: Margherita Milone; Nicola Brunetti-Pierri; Lin-Ya Tang; Neeraj Kumar; Michelle M Mezei; Keith A Josephs; Suzanne Powell; Ericka Simpson; Lee-Jun C Wong
Sensory ataxic neuropathy with ophthalmoparesis caused by POLG mutations.
Neuromuscular disorders : NMD 2008;18(8):626-32.
2008: Keith A Josephs; Wen-Lang Lin; Zeshan Ahmed; David Alexander Stroh; Neill R Graff-Radford; dennis dickson
Frontotemporal lobar degeneration with ubiquitin-positive, but TDP-43-negative inclusions.
Acta neuropathologica 2008;116(2):159-67.
2008: Keith A Josephs
Frontotemporal dementia and related disorders: deciphering the enigma.
Annals of neurology 2008;64(1):4-14.
2008: Kejal Kantarci; David S. Knopman; dennis dickson; Joseph E Parisi; Jennifer L Whitwell; Stephen D Weigand; Keith A Josephs; Bradley Boeve; Ronald C. Petersen; Clifford R Jack
Alzheimer disease: postmortem neuropathologic correlates of antemortem 1H MR spectroscopy metabolite measurements.
Radiology 2008;248(1):210-20.
2008: Hiroshige Fujishiro; Roberta Frigerio; Melinda Burnett; Kevin J Klos; Keith A Josephs; Anthony Delledonne; Joseph E Parisi; J Eric Ahlskog; dennis dickson
Cardiac sympathetic denervation correlates with clinical and pathologic stages of Parkinson's disease.
Movement disorders : official journal of the Movement Disorder Society 2008;23(8):1085-92.
2008: Christian Wider; Ryan Uitti; Zbigniew K Wszolek; John Y Fang; Keith A Josephs; Matthew C Baker; Rosa Rademakers; Michael Hutton; dennis dickson
Progranulin gene mutation with an unusual clinical and neuropathologic presentation.
Movement disorders : official journal of the Movement Disorder Society 2008;23(8):1168-73.
2008: Keith A Josephs; Jennifer L Whitwell; David S. Knopman; William T Hu; D A Stroh; M Baker; Rosa Rademakers; Bradley Boeve; Joseph E Parisi; Glenn Smith; Robert J Ivnik; Ronald C. Petersen; Clifford R Jack; dennis dickson
Abnormal TDP-43 immunoreactivity in AD modifies clinicopathologic and radiologic phenotype.
Neurology 2008;70(19 Pt 2):1850-7.
2008: dennis dickson; Hiroshige Fujishiro; Anthony DelleDonne; Joshua Menke; Zeshan Ahmed; Kevin J Klos; Keith A Josephs; Roberta Frigerio; Melinda Burnett; Joseph E Parisi; J Eric Ahlskog
Evidence that incidental Lewy body disease is pre-symptomatic Parkinson's disease.
Acta neuropathologica 2008;115(4):437-44.
2008: Keith A Josephs; Jennifer L Whitwell; Joseph E Parisi; David S. Knopman; Bradley Boeve; Yonas E Geda; Clifford R Jack; Ronald C. Petersen; dennis dickson
Argyrophilic grains: a distinct disease or an additive pathology?
Neurobiology of aging 2008;29(4):566-73.
2008: B Mark Keegan; C Giannini; Joseph E Parisi; Claudia F Lucchinetti; Bradley Boeve; Keith A Josephs
Sporadic adult-onset leukoencephalopathy with neuroaxonal spheroids mimicking cerebral MS.
Neurology 2008;70(13 Pt 2):1128-33.
2008: K Czarnecki; Neeraj Kumar; Keith A Josephs
Parkinsonism and tardive antecollis in frontotemporal dementia--increased sensitivity to newer antipsychotics?
European journal of neurology : the official journal of the European Federation of Neurological Societies 2008;15(2):199-201.
2008: Zeshan Ahmed; Keith A Josephs; John Gonzalez; Anthony DelleDonne; dennis dickson
Clinical and neuropathologic features of progressive supranuclear palsy with severe pallido-nigro-luysial degeneration and axonal dystrophy.
Brain : a journal of neurology 2008;131(Pt 2):460-72.
2008: Jennifer L Whitwell; Clifford R Jack; V Shane Pankratz; Joseph E Parisi; David S. Knopman; Bradley Boeve; Ronald C. Petersen; dennis dickson; Keith A Josephs
Rates of brain atrophy over time in autopsy-proven frontotemporal dementia and Alzheimer disease.
NeuroImage 2008;39(3):1034-40.
2008: Keith A Josephs; Jennifer L Whitwell; Zeshan Ahmed; Maria M Shiung; Stephen D Weigand; David S. Knopman; Bradley Boeve; Joseph E Parisi; Ronald C. Petersen; dennis dickson; Clifford R Jack
Beta-amyloid burden is not associated with rates of brain atrophy.
Annals of neurology 2008;63(2):204-12.
2008: Keith A Josephs; Jennifer L Whitwell; dennis dickson; Bradley Boeve; David S. Knopman; Ronald C. Petersen; Joseph E Parisi; Clifford R Jack
Voxel-based morphometry in autopsy proven PSP and CBD.
Neurobiology of aging 2008;29(2):280-9.
2008: Bradley Boeve; Keith A Josephs; Daniel A Drubach
Current and future management of the corticobasal syndrome and corticobasal degeneration.
Handbook of clinical neurology 2008;89():533-48.
2008: Keith A Josephs
Clinical aspects of TDP-43 proteinopathy, neurofilament inclusion body disease and dementias lacking distinctive proteinopathy.
Handbook of clinical neurology 2008;89():377-82.
2008: Keith A Josephs; Jennifer L Whitwell; Joseph R Duffy; W A Vanvoorst; Edythe A Strand; William T Hu; Bradley Boeve; Neill R Graff-Radford; Joseph E Parisi; David S. Knopman; dennis dickson; Clifford R Jack; Ronald C. Petersen
Progressive aphasia secondary to Alzheimer disease vs FTLD pathology.
Neurology 2008;70(1):25-34.
2008: Wendy A Vanvoorst; Melanie Greenaway; Bradley Boeve; Robert J Ivnik; Joseph E Parisi; J Eric Ahlskog; David S. Knopman; dennis dickson; Ronald C. Petersen; Glenn Smith; Keith A Josephs
Neuropsychological findings in clinically atypical autopsy confirmed corticobasal degeneration and progressive supranuclear palsy.
Parkinsonism & related disorders 2008;14(4):376-8.
2007: Keith A Josephs
Capgras syndrome and its relationship to neurodegenerative disease.
Archives of neurology 2007;64(12):1762-6.
2007: McKeon Andrew; Keith A Josephs; Kevin J Klos; Kathleen Hecksel; James H Bower; J Michael Bostwick; J Eric Ahlskog
Unusual compulsive behaviors primarily related to dopamine agonist therapy in Parkinson's disease and multiple system atrophy.
Parkinsonism & related disorders 2007;13(8):516-9.
2007: Michael D Geschwind; Keith A Josephs; Joseph E Parisi; B Mark Keegan
A 54-year-old man with slowness of movement and confusion.
Neurology 2007;69(19):1881-7.
2007: William T Hu; Jayawant N Mandrekar; Joseph E Parisi; David S. Knopman; Bradley Boeve; Ronald C. Petersen; Michael Hutton; dennis dickson; Keith A Josephs
Clinical features of pathologic subtypes of behavioral--variant frontotemporal dementia.
Archives of neurology 2007;64(11):1611-6.
2007: Keith A Josephs; dennis dickson
Hippocampal sclerosis in tau-negative frontotemporal lobar degeneration.
Neurobiology of aging 2007;28(11):1718-22.
2007: Keith A Josephs; dennis dickson
Frontotemporal lobar degeneration with upper motor neuron disease/ primary lateral sclerosis.
Neurology 2007;69(18):1800-1.
2007: William T Hu; Joseph E Parisi; David S. Knopman; Bradley Boeve; dennis dickson; J Eric Ahlskog; Ronald C. Petersen; Keith A Josephs
Clinical features and survival of 3R and 4R tauopathies presenting as behavioral variant frontotemporal dementia.
Alzheimer disease and associated disorders 2007;21(4):S39-43.
2007: Katya Rascovsky; John R Hodges; Christopher M Kipps; Julene K Johnson; William W Seeley; Mario F Mendez; David S. Knopman; Andrew Kertesz; Marek-Marsel Mesulam; David P Salmon; Douglas Galasko; Tiffany W Chow; Charles DeCarli; ARGYE HILLIS-TRUPE; Keith A Josephs; Joel H Kramer; Sandra Weintraub; Murray Grossman; Maria Luisa Gorno-Tempini; Bruce L Miller
Diagnostic criteria for the behavioral variant of frontotemporal dementia (bvFTD): current limitations and future directions.
Alzheimer disease and associated disorders 2007;21(4):S14-8.
2007: Rosa Rademakers; Matt Baker; Jennifer Gass; Jennifer Adamson; Edward D Huey; Parastoo Momeni; Salvatore Spina; Giovanni Coppola; Anna M Karydas; Heather Stewart; Nancy Johnson; Ging-Yuek Hsiung; Brendan Kelley; Karen Kuntz; Ellen Steinbart; Elisabeth McCarty Wood; Chang-En Yu; Keith A Josephs; Eric Sorenson; Kyle B Womack; Sandra Weintraub; Stuart M Pickering-Brown; Peter R Schofield; William S Brooks; Vivianna M Van Deerlin; Julie Snowden; Christopher M Clark; Andrew Kertesz; Kevin Boylan; Bernardino Ghetti; David Neary; Gerard D Schellenberg; Thomas Beach; Marek-Marsel Mesulam; D M A Mann; Jordan Grafman; Ian R Mackenzie; Howard Feldman; Thomas D Bird; Ronald C. Petersen; David S. Knopman; Bradley Boeve; Daniel Geschwind; Bruce L Miller; Zbigniew K Wszolek; Carol F Lippa; Eileen H Bigio; dennis dickson; Neill Graff-Radford; Michael Hutton
Phenotypic variability associated with progranulin haploinsufficiency in patients with the common 1477C-->T (Arg493X) mutation: an international initiative.
Lancet neurology 2007;6(10):857-68.
2007: McKeon Andrew; Sean J Pittock; Graham A Glass; Keith A Josephs; James H Bower; Vanda A Lennon; J Eric Ahlskog
Whole-body tremulousness: isolated generalized polymyoclonus.
Archives of neurology 2007;64(9):1318-22.
2007: A B Porter; L Healy; N L Foster; Keith A Josephs
Compulsive urination as a presenting symptom of frontotemporal dementia.
European journal of neurology : the official journal of the European Federation of Neurological Societies 2007;14(8):e16-7.
2007: Keith A Josephs
Frontotemporal lobar degeneration.
Neurologic clinics 2007;25(3):683-96, vi.
2007: dennis dickson; Keith A Josephs; Catalina Amador-Ortiz
TDP-43 in differential diagnosis of motor neuron disorders.
Acta neuropathologica 2007;114(1):71-9.
2007: Jennifer L Whitwell; Clifford R Jack; Kejal Kantarci; Stephen D Weigand; Bradley Boeve; David S. Knopman; Daniel A Drubach; David F Tang-Wai; Ronald C. Petersen; Keith A Josephs
Imaging correlates of posterior cortical atrophy.
Neurobiology of aging 2007;28(7):1051-61.
2007: Jennifer L Whitwell; Clifford R Jack; Joseph E Parisi; David S. Knopman; Bradley Boeve; Ronald C. Petersen; Tanis J Ferman; dennis dickson; Keith A Josephs
Rates of cerebral atrophy differ in different degenerative pathologies.
Brain : a journal of neurology 2007;130(Pt 4):1148-58.
2007: Jennifer L Whitwell; Clifford R Jack; Matthew Baker; Rosa Rademakers; Jennifer Adamson; Bradley Boeve; David S. Knopman; Joseph E Parisi; Ronald C. Petersen; dennis dickson; Michael Hutton; Keith A Josephs
Voxel-based morphometry in frontotemporal lobar degeneration with ubiquitin-positive inclusions with and without progranulin mutations.
Archives of neurology 2007;64(3):371-6.
2007: Jennifer L Whitwell; Stephen D Weigand; Maria M Shiung; Bradley Boeve; Tanis J Ferman; Glenn Smith; David S. Knopman; Ronald C. Petersen; Eduardo E Benarroch; Keith A Josephs; Clifford R Jack
Focal atrophy in dementia with Lewy bodies on MRI: a distinct pattern from Alzheimer's disease.
Brain : a journal of neurology 2007;130(Pt 3):708-19.
2007: Keith A Josephs; Zeshan Ahmed; Omi Katsuse; Joseph E Parisi; Bradley Boeve; David S. Knopman; Ronald C. Petersen; Peter Davies; Ranjan Duara; Neill R Graff-Radford; Ryan Uitti; Rosa Rademakers; Jennifer Adamson; Matthew Baker; Michael Hutton; dennis dickson
Neuropathologic features of frontotemporal lobar degeneration with ubiquitin-positive inclusions with progranulin gene (PGRN) mutations.
Journal of neuropathology and experimental neurology 2007;66(2):142-51.
2007: Bruce L Miller; Keith A Josephs; Joseph E Parisi; B Mark Keegan
A 34-year-old man with progressive behavioral and language disturbance.
Neurology 2007;68(1):68-74.
2007: Jennifer L Whitwell; Keith A Josephs
Voxel-based morphometry and its application to movement disorders.
Parkinsonism & related disorders 2007;13 Suppl 3():S406-16.
2006: Kevin J Klos; J Eric Ahlskog; Neeraj Kumar; S Cambern; John A Butz; Mary F Burritt; Robert D Fealey; Clayton T Cowl; Joseph E Parisi; Keith A Josephs
Brain metal concentrations in chronic liver failure patients with pallidal T1 MRI hyperintensity.
Neurology 2006;67(11):1984-9.
2006: Keith A Josephs; Jennifer L Whitwell; Clifford R Jack; Joseph E Parisi; dennis dickson
Frontotemporal lobar degeneration without lobar atrophy.
Archives of neurology 2006;63(11):1632-8.
2006: Bradley Boeve; Matt Baker; dennis dickson; Joseph E Parisi; Caterina Giannini; Keith A Josephs; Michael Hutton; Stuart Pickering-Brown; Rosa Rademakers; David F Tang-Wai; Clifford R Jack; Kejal Kantarci; Maria M Shiung; todd golde; Glenn Smith; Yonas E Geda; David S. Knopman; Ronald C. Petersen
Frontotemporal dementia and parkinsonism associated with the IVS1+1G->A mutation in progranulin: a clinicopathologic study.
Brain : a journal of neurology 2006;129(Pt 11):3103-14.
2006: Jennifer Gass; Ashley Cannon; Ian R A Mackenzie; Bradley Boeve; Matt Baker; Jennifer Adamson; Richard Crook; Stacey Melquist; Karen Kuntz; Ronald C. Petersen; Keith A Josephs; Stuart Pickering-Brown; Neill R Graff-Radford; Ryan Uitti; dennis dickson; Zbigniew K Wszolek; John Gonzalez; Thomas Beach; Eileen H Bigio; Nancy Johnson; Sandra Weintraub; Marek-Marsel Mesulam; Charles L White; Bryan Woodruff; Richard Caselli; Ging-Yuek Hsiung; Howard Feldman; David S. Knopman; Michael Hutton; Rosa Rademakers
Mutations in progranulin are a major cause of ubiquitin-positive frontotemporal lobar degeneration.
Human molecular genetics 2006;15(20):2988-3001.
2006: William T Hu; Joseph A Murray; Melanie Greenaway; Joseph E Parisi; Keith A Josephs
Cognitive impairment and celiac disease.
Archives of neurology 2006;63(10):1440-6.
2006: Josephine Barnes; Jennifer L Whitwell; Chris Frost; Keith A Josephs; Martin N Rossor; Nick C Fox
Measurements of the amygdala and hippocampus in pathologically confirmed Alzheimer disease and frontotemporal lobar degeneration.
Archives of neurology 2006;63(10):1434-9.
2006: Keith A Josephs; Jennifer L Whitwell; Bradley Boeve; David S. Knopman; David F Tang-Wai; Daniel A Drubach; Clifford R Jack; Ronald C. Petersen
Visual hallucinations in posterior cortical atrophy.
Archives of neurology 2006;63(10):1427-32.
2006: Kevin J Klos; M Chandler; Neeraj Kumar; J Eric Ahlskog; Keith A Josephs
Neuropsychological profiles of manganese neurotoxicity.
European journal of neurology : the official journal of the European Federation of Neurological Societies 2006;13(10):1139-41.
2006: Yasuhiko Baba; John D Putzke; Yoshio Tsuboi; Keith A Josephs; Natalie Thomas; Zbigniew K Wszolek; dennis dickson
Effect of MAPT and APOE on prognosis of progressive supranuclear palsy.
Neuroscience letters 2006;405(1-2):116-9.
2006: Graham A Glass; Keith A Josephs; J Eric Ahlskog
Respiratory insufficiency as the primary presenting symptom of multiple-system atrophy.
Archives of neurology 2006;63(7):978-81.
2006: Keith A Josephs; Joseph R Duffy; Edythe A Strand; Jennifer L Whitwell; Kenneth F Layton; Joseph E Parisi; Mary F Hauser; Robert J Witte; Bradley Boeve; David S. Knopman; dennis dickson; Clifford R Jack; Ronald C. Petersen
Clinicopathological and imaging correlates of progressive aphasia and apraxia of speech.
Brain : a journal of neurology 2006;129(Pt 6):1385-98.
2006: Ashley Cannon; Matthew Baker; Bradley Boeve; Keith A Josephs; David S. Knopman; Ronald C. Petersen; Joseph E Parisi; Dennis Dickison; Jennifer Adamson; Julie Snowden; David Neary; D M A Mann; Michael Hutton; Stuart Pickering-Brown
CHMP2B mutations are not a common cause of frontotemporal lobar degeneration.
Neuroscience letters 2006;398(1-2):83-4.
2006: Kevin J Klos; J Eric Ahlskog; Keith A Josephs; Hulya Apaydin; Joseph E Parisi; Bradley Boeve; M W DeLucia; dennis dickson
Alpha-synuclein pathology in the spinal cords of neurologically asymptomatic aged individuals.
Neurology 2006;66(7):1100-2.
2006: Keith A Josephs; Omi Katsuse; Dayne A Beccano-Kelly; Wen-Lang Lin; Ryan Uitti; Yasuhiro Fujino; Bradley Boeve; Michael Hutton; Matthew C Baker; dennis dickson
Atypical progressive supranuclear palsy with corticospinal tract degeneration.
Journal of neuropathology and experimental neurology 2006;65(4):396-405.
2006: Keith A Josephs; Joseph E Parisi; David S. Knopman; Bradley Boeve; Ronald C. Petersen; dennis dickson
Clinically undetected motor neuron disease in pathologically proven frontotemporal lobar degeneration with motor neuron disease.
Archives of neurology 2006;63(4):506-12.
2006: Tetsutaro Ozawa; Daniel G Healy; Patrick M Abou-Sleiman; Kourosh R Ahmadi; Niall Quinn; Andrew J Lees; K Shaw; Ullrich Wüllner; J Berciano; J Carsten Moller; Christoph Kamm; Katrin Burk; Keith A Josephs; Paolo Barone; Eduardo Tolosa; David B Goldstein; Gregor Wenning; Felix Geser; Janice L Holton; Thomas Gasser; Tamas Revesz; Nicholas W Wood
The alpha-synuclein gene in multiple system atrophy.
Journal of neurology, neurosurgery, and psychiatry 2006;77(4):464-7.
2006: Keith A Josephs; Joseph Y Matsumoto; J Eric Ahlskog
Benign tremulous parkinsonism.
Archives of neurology 2006;63(3):354-7.
2006: Keith A Josephs; Jayawant N Mandrekar; dennis dickson
The relationship between histopathological features of progressive supranuclear palsy and disease duration.
Parkinsonism & related disorders 2006;12(2):109-12.
2006: B A Crum; Keith A Josephs
Varied electrophysiologic patterns in spinocerebellar ataxia type 2.
European journal of neurology : the official journal of the European Federation of Neurological Societies 2006;13(2):194-7.
2006: Jennifer L Whitwell; Clifford R Jack; Matthew L Senjem; Keith A Josephs
Patterns of atrophy in pathologically confirmed FTLD with and without motor neuron degeneration.
Neurology 2006;66(1):102-4.
2006: Keith A Josephs; Ronald C. Petersen; David S. Knopman; Bradley Boeve; Jennifer L Whitwell; Joseph R Duffy; Joseph E Parisi; dennis dickson
Clinicopathologic analysis of frontotemporal and corticobasal degenerations and PSP.
Neurology 2006;66(1):41-8.
2006: Hema R Murali; Keith A Josephs; Eelco F M Wijdicks
Guillain-Barré syndrome in an immunocompromised patient and coccidioidomycosis infection.
Reviews in neurological diseases 2006;3(2):82-4.
2006: Basil Ridha; Keith A Josephs
Young-onset dementia: a practical approach to diagnosis.
The neurologist 2006;12(1):2-13.
2006: A Shamim; B K Siddiqui; Keith A Josephs
The corticobasal syndrome triggered by central pontine myelinolysis.
European journal of neurology : the official journal of the European Federation of Neurological Societies 2006;13(1):82-4.
2006: Keith A Josephs; Jennifer L Whitwell; Bradley Boeve; Maria M Shiung; Jeffrey L Gunter; Joseph E Parisi; dennis dickson; Clifford R Jack
Rates of cerebral atrophy in autopsy-confirmed progressive supranuclear palsy.
Annals of neurology 2006;59(1):200-3.
2005: Kevin J Klos; Keith A Josephs; Joseph E Parisi; dennis dickson
Alpha-synuclein immunohistochemistry in two cases of co-occurring idiopathic Parkinson's disease and motor neuron disease.
Movement disorders : official journal of the Movement Disorder Society 2005;20(11):1515-20.
2005: Jennifer L Whitwell; Keith A Josephs; Martin N Rossor; John M Stevens; Tamas Revesz; Janice L Holton; Safa Al-Sarraj; Alison K Godbolt; Nick C Fox; Jason D Warren
Magnetic resonance imaging signatures of tissue pathology in frontotemporal dementia.
Archives of neurology 2005;62(9):1402-8.
2005: Kevin J Klos; J Eric Ahlskog; Keith A Josephs; Robert D Fealey; Clayton T Cowl; Neeraj Kumar
Neurologic spectrum of chronic liver failure and basal ganglia T1 hyperintensity on magnetic resonance imaging: probable manganese neurotoxicity.
Archives of neurology 2005;62(9):1385-90.
2005: Kevin J Klos; James H Bower; Keith A Josephs; Joseph Y Matsumoto; J Eric Ahlskog
Pathological hypersexuality predominantly linked to adjuvant dopamine agonist therapy in Parkinson's disease and multiple system atrophy.
Parkinsonism & related disorders 2005;11(6):381-6.
2005: M Leann Dodd; Kevin J Klos; James H Bower; Yonas E Geda; Keith A Josephs; J Eric Ahlskog
Pathological gambling caused by drugs used to treat Parkinson disease.
Archives of neurology 2005;62(9):1377-81.
2005: Keith A Josephs; David S. Knopman; Jennifer L Whitwell; Bradley Boeve; Joseph E Parisi; Ronald C. Petersen; dennis dickson
Survival in two variants of tau-negative frontotemporal lobar degeneration: FTLD-U vs FTLD-MND.
Neurology 2005;65(4):645-7.
2005: B H Ridha; Keith A Josephs; Martin N Rossor
Delusions and hallucinations in dementia with Lewy bodies: worsening with memantine.
Neurology 2005;65(3):481-2.
2005: Keith A Josephs; Bradley Boeve; Joseph R Duffy; Glenn Smith; David S. Knopman; Joseph E Parisi; Ronald C. Petersen; dennis dickson
Atypical progressive supranuclear palsy underlying progressive apraxia of speech and nonfluent aphasia.
Neurocase 2005;11(4):283-96.
2005: Yoshio Tsuboi; Keith A Josephs; Bradley Boeve; Irene Litvan; Richard Caselli; John Caviness; Ryan Uitti; Allen D Bott; dennis dickson
Increased tau burden in the cortices of progressive supranuclear palsy presenting with corticobasal syndrome.
Movement disorders : official journal of the Movement Disorder Society 2005;20(8):982-8.
2005: Alison K Godbolt; Keith A Josephs; Tamas Revesz; Elizabeth K Warrington; Peter Lantos; Andrew King; Nick C Fox; Safa Al-Sarraj; Janice Holton; Lisa Cipolotti; M Nadeem Khan; Martin N Rossor
Sporadic and familial dementia with ubiquitin-positive tau-negative inclusions: clinical features of one histopathological abnormality underlying frontotemporal lobar degeneration.
Archives of neurology 2005;62(7):1097-101.
2005: William T Hu; Keith A Josephs; J Eric Ahlskog; Cheolsu Shin; Bradley Boeve; Robert J Witte
MRI correlates of alien leg-like phenomenon in corticobasal degeneration.
Movement disorders : official journal of the Movement Disorder Society 2005;20(7):870-3.
2005: Keith A Josephs; J Eric Ahlskog; Kevin J Klos; Neeraj Kumar; Robert D Fealey; Max R Trenerry; Clayton T Cowl
Neurologic manifestations in welders with pallidal MRI T1 hyperintensity.
Neurology 2005;64(12):2033-9.
2005: G A Rippon; Bradley Boeve; Joseph E Parisi; dennis dickson; Robert J Ivnik; Clifford R Jack; Michael Hutton; M Baker; Keith A Josephs; David S. Knopman; Ronald C. Petersen
Late-onset frontotemporal dementia associated with progressive supranuclear palsy/argyrophilic grain disease/Alzheimer's disease pathology.
Neurocase 2005;11(3):204-11.
2005: Matt Stead; Keith A Josephs
Successful treatment of status migrainosus after electroconvulsive therapy with dihydroergotamine.
Headache 2005;45(4):378-80.
2005: Brandy R Matthews; Lyell K Jones; Dahlia A Saad; Allen J Aksamit; Keith A Josephs
Cerebellar ataxia and central nervous system whipple disease.
Archives of neurology 2005;62(4):618-20.
2005: David S. Knopman; Bradley Boeve; Joseph E Parisi; dennis dickson; Glenn Smith; Robert J Ivnik; Keith A Josephs; Ronald C. Petersen
Antemortem diagnosis of frontotemporal lobar degeneration.
Annals of neurology 2005;57(4):480-8.
2005: Keith A Josephs; Hirotake Uchikado; Rodney D McComb; Rifaat Bashir; Zbigniew K Wszolek; Jerry Swanson; Joseph Matsumoto; Gerry Shaw; dennis dickson
Extending the clinicopathological spectrum of neurofilament inclusion disease.
Acta neuropathologica 2005;109(4):427-32.
2005: John C Janssen; Jonathan M Schott; Lisa Cipolotti; Nick C Fox; Rachael I Scahill; Keith A Josephs; John M Stevens; Martin N Rossor
Mapping the onset and progression of atrophy in familial frontotemporal lobar degeneration.
Journal of neurology, neurosurgery, and psychiatry 2005;76(2):162-8.
2004: Keith A Josephs; Joseph Y Matsumoto; Noralane M Lindor
Heterozygous Niemann-Pick disease type C presenting with tremor.
Neurology 2004;63(11):2189-90.
2004: Keith A Josephs; David F Tang-Wai; Steven D Edland; David S. Knopman; dennis dickson; Joseph E Parisi; Ronald C. Petersen; Clifford R Jack; Bradley Boeve
Correlation between antemortem magnetic resonance imaging findings and pathologically confirmed corticobasal degeneration.
Archives of neurology 2004;61(12):1881-4.
2004: Tetsutaro Ozawa; Dominic C Paviour; Niall Quinn; Keith A Josephs; Hardev Sangha; Linda Kilford; Daniel G Healy; Nicholas W Wood; Andrew J Lees; Janice L Holton; Tamas Revesz
The spectrum of pathological involvement of the striatonigral and olivopontocerebellar systems in multiple system atrophy: clinicopathological correlations.
Brain : a journal of neurology 2004;127(Pt 12):2657-71.
2004: Keith A Josephs; Michael H Silber; Robert D Fealey; Todd B Nippoldt; Raymond G Auger; Steven Vernino
Neurophysiologic studies in Morvan syndrome.
Journal of clinical neurophysiology : official publication of the American Electroencephalographic Society 2004;21(6):440-5.
2004: Dominic C Paviour; Andrew J Lees; Keith A Josephs; Tetsutaro Ozawa; Milan Ganguly; Catherine Strand; Alison K Godbolt; Robin S Howard; Tamas Revesz; Janice L Holton
Frontotemporal lobar degeneration with ubiquitin-only-immunoreactive neuronal changes: broadening the clinical picture to include progressive supranuclear palsy.
Brain : a journal of neurology 2004;127(Pt 11):2441-51.
2004: Keith A Josephs; Yoshio Tsuboi; Natalie Cookson; Hilary Watt; dennis dickson
Apolipoprotein E epsilon 4 is a determinant for Alzheimer-type pathologic features in tauopathies, synucleinopathies, and frontotemporal degeneration.
Archives of neurology 2004;61(10):1579-84.
2004: Keith A Josephs; Janice L Holton; Martin N Rossor; Alison K Godbolt; Tetsutaro Ozawa; K Strand; N Khan; Safa Al-Sarraj; Tamas Revesz
Frontotemporal lobar degeneration and ubiquitin immunohistochemistry.
Neuropathology and applied neurobiology 2004;30(4):369-73.
2004: Keith A Josephs; Frank A Rubino; dennis dickson
Nonvasculitic autoimmune inflammatory meningoencephalitis.
Neuropathology : official journal of the Japanese Society of Neuropathology 2004;24(2):149-52.
2004: Keith A Josephs; Yoshio Tsuboi; dennis dickson
Creutzfeldt-Jakob disease presenting as progressive supranuclear palsy.
European journal of neurology : the official journal of the European Federation of Neurological Societies 2004;11(5):343-6.
2004: Jennifer L Whitwell; Jason D Warren; Keith A Josephs; Alison K Godbolt; Tamas Revesz; Nick C Fox; Martin N Rossor
Voxel-based morphometry in tau-positive and tau-negative frontotemporal lobar degenerations.
Neuro-degenerative diseases 2004;1(4-5):225-30.
2004: Keith A Josephs; A G Jones; dennis dickson
Hippocampal sclerosis and ubiquitin-positive inclusions in dementia lacking distinctive histopathology.
Dementia and geriatric cognitive disorders 2004;17(4):342-5.
2003: David F Tang-Wai; Keith A Josephs; Bradley Boeve; dennis dickson; Joseph E Parisi; Ronald C. Petersen
Pathologically confirmed corticobasal degeneration presenting with visuospatial dysfunction.
Neurology 2003;61(8):1134-5.
2003: Keith A Josephs; Janice L Holton; Martin N Rossor; Hans Braendgaard; Tetsutaro Ozawa; Nick C Fox; Ronald C. Petersen; Gary S Pearl; Milan Ganguly; Pedro Rosa; Henning Laursen; Joseph E Parisi; Gunhild Waldemar; Niall Quinn; dennis dickson; Tamas Revesz
Neurofilament inclusion body disease: a new proteinopathy?
Brain : a journal of neurology 2003;126(Pt 10):2291-303.
2003: Keith A Josephs; dennis dickson
Diagnostic accuracy of progressive supranuclear palsy in the Society for Progressive Supranuclear Palsy brain bank.
Movement disorders : official journal of the Movement Disorder Society 2003;18(9):1018-26.
2003: Y Tsuboi; J Slowinski; Keith A Josephs; William Honer; Zbigniew K Wszolek; dennis dickson
Atrophy of superior cerebellar peduncle in progressive supranuclear palsy.
Neurology 2003;60(11):1766-9.
2003: Keith A Josephs; D F Tang Wai; Joseph E Parisi
Hippocampal sclerosis in a case of Alzheimer's disease-like dementia with late onset intractable epilepsy.
European journal of neurology : the official journal of the European Federation of Neurological Societies 2003;10(3):333-4.
2003: Keith A Josephs; M W Van Gerpen; J A Van Gerpen
Adult onset Niemann-Pick disease type C presenting with psychosis.
Journal of neurology, neurosurgery, and psychiatry 2003;74(4):528-9.
2003: David F Tang-Wai; Keith A Josephs; Bradley Boeve; Ronald C. Petersen; Joseph E Parisi; dennis dickson
Coexistent Lewy body disease in a case of "visual variant of Alzheimer's disease".
Journal of neurology, neurosurgery, and psychiatry 2003;74(3):389.
2003: Yoshio Tsuboi; Keith A Josephs; Natalie Cookson; dennis dickson
APOE E4 is a determinant for Alzheimer type pathology in progressive supranuclear palsy.
Neurology 2003;60(2):240-5.
2002: Keith A Josephs; Takashi Ishizawa; Yoshio Tsuboi; Natalie Cookson; dennis dickson
A clinicopathological study of vascular progressive supranuclear palsy: a multi-infarct disorder presenting as progressive supranuclear palsy.
Archives of neurology 2002;59(10):1597-601.
2002: Keith A Josephs; Joseph E Parisi; dennis dickson
Alpha-synuclein studies are negative in postencephalic parkinsonism of von Economo.
Neurology 2002;59(4):645-6.
2001: L H Travis; Keith A Josephs; J H Bower
25-year-old woman with incoordination and decreased balance.
Mayo Clinic proceedings. Mayo Clinic 2001;76(5):551-4.